Schwannomas are histologically benign tumors seen along the course of peripheral nerves, nerve roots, and cranial nerves [especially cranial nerve V (trigeminal) and VIII (vestibulocochlear)]. They may occur in isolation or in association with neurofibromatosis. They arise from the Schwann cells that create the myelin sheath around peripheral nerves. They result in symptoms when they disrupt the function of the nerve from which they arise, or cause mass effect on adjacent structures. In this case, symptoms resulted from compression of the high cervical spinal cord when the Schwannoma grew along the C1 nerve root through the intervertebral foramen.