INTESTINAL INFECTIOUS DISEASES (001-009)
Amebic abscess of brain
(and liver) (and lung)
Includes: infection by Mycobacterium tuberculosis
(human) (bovine)
Excludes: congenital tuberculosis (771.2)
late effects of tuberculosis (137.0-137.4)
The following fifth-digit
subclassification is for use with categories 010-018:
0 unspecified
1 bacteriological or histological examination not done
2 bacteriological or histological examination
unknown (at present)
3 tubercle bacilli found (in sputum) by microscopy
4 tubercle bacilli not found (in sputum) by microscopy, but found by
bacterial culture
5 tubercle bacilli not found by bacteriological examination, but
tuberculosis confirmed histologically
6 tubercle bacilli not found by bacteriological
or histological examination, but tuberculosis confirmed by other methods
[inoculation of animals]
Requires
fifth digit. See beginning of
section 010-018 for codes and definitions.
Tuberculosis of meninges
(cerebral) (spinal)
Tuberculous:
leptomeningitis
meningoencephalitis
Excludes: tuberculoma
of meninges (013.1)
Tuberculosis of brain
(current disease)
013.3 Tuberculous abscess of brain
013.4 Tuberculoma of spinal cord
013.5 Tuberculous abscess of spinal cord
013.6 Tuberculous encephalitis or myelitis
013.8 Other specified tuberculosis of central nervous system
013.9 Unspecified tuberculosis of central nervous system
Tuberculosis of central nervous system NOS
036.0 Meningococcal meningitis
Cerebrospinal fever
(meningococcal)
Meningitis:
cerebrospinal
epidemic
036.1 Meningococcal encephalitis
Meningococcal septicemia
Excludes: tetanus:
complicating:
abortion (634-638 with .0, 639.0)
ectopic or molar pregnancy (639.0)
neonatorum (771.3)
HUMAN IMMUNODEFICIENCY VIRUS (HIV) INFECTION (042)
Acquired immune deficiency
syndrome
Acquired immunodeficiency
syndrome
AIDS
AIDS-like syndrome
AIDS-related complex
ARC
HIV infection, symptomatic
Use additional code(s) to
identify all manifestations of HIV
Use additional code to
identify HIV-2 infection (079.53)
Excludes: asymptomatic
HIV infection status (V08)
exposure to HIV virus (V01.79)
nonspecific serologic evidence of HIV (795.71)
POLIOMYELITIS AND OTHER NON-ARTHROPOD-BORNE VIRAL DISEASES OF CENTRAL NERVOUS SYSTEM (045-049)
Excludes: late
effects of acute poliomyelitis (138)
The following fifth-digit
subclassification is for use with category 045:
0 poliovirus, unspecified type
1 poliovirus type I
2 poliovirus type II
3 poliovirus type III
045.0 Acute paralytic poliomyelitis specified as bulbar
Infantile paralysis (acute)
specified as bulbar
Poliomyelitis (acute)
(anterior) specified as bulbar
Polioencephalitis (acute)
(bulbar)
Polioencephalomyelitis
(acute) (anterior) (bulbar)
045.1 Acute poliomyelitis with other paralysis
Paralysis:
acute atrophic, spinal
infantile, paralytic
Poliomyelitis (acute) with
paralysis except bulbar
anterior with paralysis except bulbar
epidemic with paralysis except bulbar
045.2 Acute nonparalytic poliomyelitis
Poliomyelitis (acute)
specified as nonparalytic
anterior specified as nonparalytic
epidemic specified as nonparalytic
045.9 Acute poliomyelitis, unspecified
Infantile paralysis
unspecified whether paralytic or nonparalytic
Poliomyelitis (acute)
unspecified whether paralytic or nonparalytic
anterior unspecified whether paralytic or nonparalytic
epidemic unspecified whether paralytic or nonparalytic
046.1 Jakob-Creutzfeldt disease
Subacute spongiform
encephalopathy
046.2 Subacute sclerosing panencephalitis
Dawson's inclusion body
encephalitis
Van Bogaert's sclerosing
leukoencephalitis
046.3 Progressive multifocal leukoencephalopathy
Multifocal
leukoencephalopathy NOS
046.8 Other specified slow virus infection of central nervous system
046.9 Unspecified slow virus infection of central nervous system
Includes: meningitis:
abacterial
aseptic
viral
Excludes: meningitis
due to:
adenovirus (049.1)
arthropod-borne virus (060.0-066.9)
leptospira (100.81)
virus of:
herpes simplex (054.72)
herpes zoster (053.0)
lymphocytic choriomeningitis (049.0)
mumps (072.1)
poliomyelitis (045.0-045.9)
any other infection specifically classified elsewhere
Meningo-eruptive syndrome
047.8 Other specified viral meningitis
047.9 Unspecified viral meningitis
Viral meningitis NOS
Excludes: late
effects of viral encephalitis (139.0)
049.0 Lymphocytic choriomeningitis
Lymphocytic:
meningitis (serous) (benign)
meningoencephalitis (serous) (benign)
049.1 Meningitis due to adenovirus
049.8 Other specified non-arthropod-borne viral diseases of central nervous system
Encephalitis:
acute:
inclusion body
necrotizing
epidemic
lethargica
Rio Bravo
von
Economo's disease
049.9 Unspecified non-arthropod-borne viral diseases of central nervous system
Viral encephalitis NOS
VIRAL DISEASES ACCOMPANIED BY EXANTHEM (050-057)
Excludes: arthropod-borne viral diseases (060.0-066.9)
Boston exanthem (048)
Includes: shingles
zona
053.1 With other nervous system complications
053.10 With unspecified nervous system complication
053.11 Geniculate herpes zoster
Herpetic geniculate
ganglionitis
053.12 Postherpetic trigeminal neuralgia
053.13 Postherpetic polyneuropathy
053.2 With ophthalmic complications
053.20 Herpes zoster dermatitis of eyelid
Herpes zoster ophthalmicus
053.21 Herpes zoster keratoconjunctivitis
053.22 Herpes zoster iridocyclitis
054.3 Herpetic meningoencephalitis
Herpes encephalitis
Simian B disease
056.0 With neurological complications
056.00 With unspecified neurological complication
056.01 Encephalomyelitis due to rubella
Encephalitis due to rubella
Meningoencephalitis due to
rubella
Use additional code to
identify any associated meningitis (321.2)
Excludes: late effects of viral encephalitis (139.0)
Japanese B encephalitis
062.1 Western equine encephalitis
062.2 Eastern equine encephalitis
Excludes: Venezuelan
equine encephalitis (066.2)
Australian arboencephalitis
Australian X disease
Murray Valley encephalitis
062.5 California virus encephalitis
Encephalitis:
California
La Crosse
Tahyna fever
062.8 Other specified mosquito-borne viral encephalitis
Encephalitis by Ilheus
virus
Excludes: West Nile
virus (066.40-066.49)
062.9 Mosquito-borne viral encephalitis, unspecified
Includes: diphasic meningoencephalitis
063.0 Russian spring-summer [taiga] encephalitis
063.2 Central European encephalitis
063.8 Other specified tick-borne viral encephalitis
Langat encephalitis
Powassan encephalitis
063.9 Tick-borne viral encephalitis, unspecified
Arthropod-borne viral
encephalitis, vector unknown
Negishi virus encephalitis
Excludes: viral
encephalitis NOS (049.9)
066.40 West Nile fever, unspecified
West Nile fever NOS
West Nile fever without
complications
West Nile virus NOS
066.41 West Nile fever with encephalitis
West Nile encephalitis
West Nile encephalomyelitis
066.42 West Nile fever with other neurologic manifestation
Use additional code to
specify the neurologic manifestation
Use additional code to
identify any associated mental disorder
Locomotor ataxia
(progressive)
Posterior spinal sclerosis
(syphilitic)
Tabetic neurosyphilis
Use additional code to
identify manifestation, as:
neurogenic arthropathy [Charcot's joint disease] (713.5)
Dementia paralytica
General paralysis (of the insane)
(progressive)
Paretic neurosyphilis
Taboparesis
Meningovascular syphilis
Excludes: acute
syphilitic meningitis (secondary) (091.81)
094.3 Asymptomatic neurosyphilis
094.8 Other specified neurosyphilis
094.81 Syphilitic encephalitis
094.82 Syphilitic Parkinsonism
094.83 Syphilitic disseminated retinochoroiditis
094.84 Syphilitic optic atrophy
094.85 Syphilitic retrobulbar neuritis
094.86 Syphilitic acoustic neuritis
094.87 Syphilitic ruptured cerebral aneurysm
094.9 Neurosyphilis, unspecified
Gumma (syphilitic) of
central nervous system NOS
Syphilis (early) (late) of
central nervous system NOS
Syphiloma of central nervous system NOS
MYCOSES (110-118)
Use additional code to
identify manifestation, as:
arthropathy (711.6)
meningitis
(321.0-321.1)
otitis externa
(380.15)
Excludes: infection by Actinomycetales, such as species of Actinomyces,
Actinomadura, Nocardia, Streptomyces (039.0-039.9)
The following fifth-digit
subclassification is for use with category 115:
0 without mention of manifestation
1 meningitis
2 retinitis
3 pericarditis
4 endocarditis
5 pneumonia
9 other
115.0 Infection by Histoplasma capsulatum
American histoplasmosis
Darling's disease
Reticuloendothelial
cytomycosis
Small form histoplasmosis
115.1 Infection by Histoplasma duboisii
African histoplasmosis
Large form histoplasmosis
115.9 Histoplasmosis, unspecified
Histoplasmosis NOS
Infection by Aspergillus
species, mainly A. fumigatus, A. flavus group, A. terreus group
Trichinella spiralis
infection
Trichinellosis
Trichiniasis
Includes: infection by toxoplasma gondii
toxoplasmosis (acquired)
Excludes: congenital
toxoplasmosis (771.2)
130.0 Meningoencephalitis due to toxoplasmosis
Encephalitis due to
acquired toxoplasmosis
Besnier-Boeck-Schaumann
disease
Lupoid (miliary) of Boeck
Lupus pernio (Besnier)
Lymphogranulomatosis,
benign (Schaumann's)
Sarcoid (any site):
NOS
Boeck
Darier-Roussy
Uveoparotid fever
136.2 Specific infections by free-living amebae
Meningoencephalitis due to
Naegleria
Note: This category is to be used to indicate
conditions classifiable to 010-018 as the cause of late effects, which are themselves classified elsewhere. The "late
effects" include those specified as such, as sequelae, or as due to old or
inactive tuberculosis, without evidence of active disease.
137.1 Late effects of central nervous system tuberculosis
Note: This category is to be used to indicate
conditions classifiable to 045 as the cause of late effects, which are themselves classified elsewhere. The "late effects" include
conditions specified as such, or as sequelae, or as due to old or inactive
poliomyelitis, without evidence of active disease.
Note: This category is to be used to indicate
conditions classifiable to categories 001-009, 020-041, 046-136 as the cause of
late effects, which are themselves classified
elsewhere. The "late effects"
include conditions specified as such; they also include sequela of diseases
classifiable to the above categories if there is evidence that the disease
itself is no longer present.
139.0 Late effects of viral encephalitis
Late effects of conditions
classifiable to 049.8-049.9, 062-064
170.2 Vertebral column, excluding sacrum and coccyx
Spinal column
Spine
Vertebra
Excludes: sacrum
and coccyx (170.6)
170.6 Pelvic bones, sacrum, and coccyx
Coccygeal vertebra
Ilium
Ischium
Pubic bone
Sacral vertebra
Excludes: cranial
nerves (192.0)
retrobulbar area (190.1)
191.0 Cerebrum, except lobes and ventricles
Basal ganglia
Cerebral cortex
Corpus striatum
Globus pallidus
Hypothalamus
Thalamus
Hippocampus
Uncus
Choroid plexus
Floor of ventricle
Cerebellopontine angle
Cerebral peduncle
Medulla oblongata
Midbrain
Pons
Corpus callosum
Tapetum
Malignant neoplasm of
contiguous or overlapping sites of brain whose point of origin cannot be
determined
Cranial fossa NOS
Excludes: peripheral,
sympathetic, and parasympathetic nerves and ganglia (171.0-171.9)
Olfactory bulb
Dura (mater)
Falx (cerebelli) (cerebri)
Meninges NOS
Tentorium
Cauda equina
192.8 Other specified sites of nervous system
Malignant neoplasm of
contiguous or overlapping sites of other parts of nervous system whose point of
origin cannot be determined
192.9 Nervous system, part unspecified
Nervous system (central)
NOS
Excludes: meninges
NOS (192.1)
198.4 Other parts of nervous system
Meninges (cerebral)
(spinal)
Excludes: hemangioma
(228.02)
neurofibromatosis (237.7)
peripheral, sympathetic, and parasympathetic nerves and ganglia
(215.0-215.9)
retrobulbar (224.1)
Meninges NOS
Meningioma (cerebral)
Cauda equina
Spinal meningioma
225.8 Other specified sites of nervous system
225.9 Nervous system, part unspecified
Nervous system (central)
NOS
Excludes: meninges
NOS (225.2)
227.3 Pituitary gland and craniopharyngeal duct (pouch)
Craniobuccal pouch
Hypophysis
Rathke's pouch
Sella turcica
Pineal body
Includes: angioma (benign) (cavernous)
(congenital) NOS
cavernous nevus
glomus tumor
hemangioma (benign) (congenital)
Excludes: benign
neoplasm of spleen, except hemangioma and lymphangioma (211.9)
glomus jugulare (227.6)
nevus:
NOS (216.0-216.9)
blue or pigmented (216.0-216.9)
vascular (757.32)
228.02 Of intracranial structures
DISEASES OF OTHER ENDOCRINE GLANDS (250-259)
Excludes: gestational
diabetes (648.8)
hyperglycemia NOS (790.6)
neonatal diabetes mellitus (775.1)
nonclinical diabetes (790.29)
The following fifth-digit
subclassification is for use with category 250:
0 type II or unspecified type, not stated as uncontrolled
Fifth-digit 0 is for use
for type II patients, even if the patient requires insulin
Use additional
code, if applicable, for associated long-term (current) insulin use V58.67
1 type I [juvenile type], not stated as uncontrolled
2 type II or unspecified type, uncontrolled
Use additional
code, if applicable, for associated long-term (current) insulin use V58.67
Fifth-digit 2 is for use
for type II, adult-onset, diabetic patients, even if the patient requires
insulin
3 type I [juvenile type], uncontrolled
250.0 Diabetes mellitus without mention of complication
Diabetes mellitus without
mention of complication or manifestation classifiable to 250.1-250.9
Diabetes (mellitus) NOS
Diabetic:
acidosis without mention of coma
ketosis without mention of coma
250.2 Diabetes with hyperosmolarity
Hyperosmolar (nonketotic)
coma
250.3 Diabetes with other coma
Diabetic coma (with
ketoacidosis)
Diabetic hypoglycemic coma
Insulin coma NOS
Excludes: diabetes
with hyperosmolar coma (250.2)
250.6 Diabetes with neurological manifestations
Use additional code to
identify manifestation, as:
diabetic:
amyotrophy (358.1)
gastroparalysis (536.3)
gastroparesis (536.3)
mononeuropathy (354.0-355.9)
neurogenic arthropathy (713.5)
peripheral autonomic neuropathy (337.1)
polyneuropathy (357.2)
Parathyroiditis (autoimmune)
Tetany:
parathyroid
parathyroprival
Excludes: pseudohypoparathyroidism
(275.49)
pseudopseudohypoparathyroidism (275.49)
tetany NOS (781.7)
transitory neonatal hypoparathyroidism (775.4)
Includes: the listed conditions whether the
disorder is in the pituitary or the hypothalamus
Excludes: Cushing's
syndrome (255.0)
253.0 Acromegaly and gigantism
Overproduction of growth
hormone
Cachexia, pituitary
Necrosis of pituitary
(postpartum)
Pituitary insufficiency NOS
Sheehan's syndrome
Simmonds' disease
Excludes: iatrogenic
hypopituitarism (253.7)
Vasopressin deficiency
Excludes: nephrogenic
diabetes insipidus (588.1)
253.8 Other disorders of the pituitary and other syndromes of diencephalohypophyseal origin
Abscess of pituitary
Adiposogenital dystrophy
Cyst of Rathke's pouch
Fröhlich's syndrome
Excludes: craniopharyngioma
(237.0)
Dyspituitarism
Excludes: aplasia
or dysplasia with immunodeficiency (279.2)
hypoplasia with immunodeficiency (279.2)
myasthenia gravis (358.00-358.01)
254.0 Persistent hyperplasia of thymus
Hypertrophy of thymus
254.8 Other specified diseases of thymus gland
Atrophy of thymus
Cyst of thymus
Excludes: thymoma
(212.6)
254.9 Unspecified disease of thymus gland
Excludes: deficiency anemias (280.0-281.9)
265.1 Other and unspecified manifestations of thiamine deficiency
Other vitamin B1 deficiency
states
Deficiency:
niacin (-tryptophan)
nicotinamide
nicotinic acid
vitamin PP
Pellagra (alcoholic)
Riboflavin [vitamin B2] deficiency
Deficiency:
pyridoxal
pyridoxamine
pyridoxine
Vitamin B6 deficiency
syndrome
Excludes: vitamin
B6-responsive sideroblastic anemia (285.0)
266.2 Other B-complex deficiencies
Deficiency:
cyanocobalamin
folic acid
vitamin B12
Excludes: combined
system disease with anemia (281.0-281.1)
deficiency anemias (281.0-281.9)
subacute degeneration of spinal cord with anemia (281.0-281.1)
Excludes: vitamin
D-resistant:
osteomalacia (275.3)
rickets (275.3)
Excludes: celiac
rickets (579.0)
renal rickets (588.0)
Any condition specified as
due to rickets and stated to be a late effect or sequela of rickets
Use additional code to
identify the nature of late effect
268.2 Osteomalacia, unspecified
268.9 Unspecified vitamin D deficiency
Avitaminosis D
Use additional code to
identify any associated mental retardation
Excludes: abnormal
findings without manifest disease (790.0-796.9)
disorders of purine and pyrimidine metabolism (277.1-277.2)
gout (274.0-274.9)
270.0 Disturbances of amino-acid transport
Cystinosis
Cystinuria
Fanconi (-de Toni) (-Debré)
syndrome
Glycinuria (renal)
Hartnup disease
Hyperphenylalaninemia
270.2 Other disturbances of aromatic amino-acid metabolism
Albinism
Alkaptonuria
Alkaptonuric ochronosis
Disturbances of metabolism
of tyrosine and tryptophan
Homogentisic acid defects
Hydroxykynureninuria
Hypertyrosinemia
Indicanuria
Kynureninase defects
Oasthouse urine disease
Ochronosis
Tyrosinosis
Tyrosinuria
Waardenburg syndrome
Excludes: vitamin
B6-deficiency syndrome (266.1)
270.3 Disturbances of branched-chain amino-acid metabolism
Disturbances of metabolism
of leucine, isoleucine, and valine
Hypervalinemia
Intermittent branched-chain
ketonuria
Leucine-induced
hypoglycemia
Leucinosis
Maple syrup urine disease
270.4 Disturbances of sulphur-bearing amino-acid metabolism
Cystathioninemia
Cystathioninuria
Disturbances of metabolism
of methionine, homocystine, and cystathionine
Homocystinuria
Hypermethioninemia
Methioninemia
270.5 Disturbances of histidine metabolism
Carnosinemia
Histidinemia
Hyperhistidinemia
Imidazole aminoaciduria
270.6 Disorders of urea cycle metabolism
Argininosuccinic aciduria
Citrullinemia
Disorders of metabolism of
ornithine, citrulline, argininosuccinic acid, arginine, and ammonia
Hyperammonemia
Hyperornithinemia
270.7 Other disturbances of straight-chain amino-acid metabolism
Glucoglycinuria
Glycinemia (with
methylmalonic acidemia)
Hyperglycinemia
Hyperlysinemia
Pipecolic acidemia
Saccharopinuria
Other disturbances of
metabolism of glycine, threonine, serine, glutamine, and lysine
270.8 Other specified disorders of amino-acid metabolism
Alaninemia
Ethanolaminuria
Glycoprolinuria
Hydroxyprolinemia
Hyperprolinemia
Iminoacidopathy
Prolinemia
Prolinuria
Sarcosinemia
270.9 Unspecified disorder of amino-acid metabolism
Excludes: abnormality
of secretion of glucagon (251.4)
diabetes mellitus (250.0-250.9)
hypoglycemia NOS (251.2)
mucopolysaccharidosis (277.5)
Amylopectinosis
Glucose-6-phosphatase
deficiency
Glycogen storage disease
McArdle's disease
Pompe's disease
von
Gierke's disease
Galactose-1-phosphate
uridyl transferase deficiency
Galactosuria
271.2 Hereditary fructose intolerance
Essential benign
fructosuria
Fructosemia
271.3 Intestinal disaccharidase deficiencies and disaccharide malabsorption
Intolerance or
malabsorption (congenital) (of):
glucose-galactose
lactose
sucrose-isomaltose
Renal diabetes
271.8 Other specified disorders of carbohydrate transport and metabolism
Essential benign pentosuria
Fucosidosis
Glycolic aciduria
Hyperoxaluria (primary)
Mannosidosis
Oxalosis
Xylosuria
Xylulosuria
271.9 Unspecified disorder of carbohydrate transport and metabolism
Excludes: localized
cerebral lipidoses (330.1)
272.0 Pure hypercholesterolemia
Familial
hypercholesterolemia
Fredrickson Type IIa
hyperlipoproteinemia
Hyperbetalipoproteinemia
Hyperlipidemia, Group A
Low-density-lipoid-type
[LDL] hyperlipoproteinemia
Endogenous
hyperglyceridemia
Fredrickson Type IV
hyperlipoproteinemia
Hyperlipidemia, Group B
Hyperprebetalipoproteinemia
Hypertriglyceridemia,
essential
Very-low-density-lipoid-type
[VLDL] hyperlipoproteinemia
Broad- or
floating-betalipoproteinemia
Fredrickson Type IIb or III
hyperlipoproteinemia
Hypercholesterolemia with
endogenous hyperglyceridemia
Hyperbetalipoproteinemia
with prebetalipoproteinemia
Tubo-eruptive xanthoma
Xanthoma tuberosum
Bürger-Grütz syndrome
Fredrickson type I or V
hyperlipoproteinemia
Hyperlipidemia, Group D
Mixed hyperglyceridemia
272.4 Other and unspecified hyperlipidemia
Alpha-lipoproteinemia
Combined hyperlipidemia
Hyperlipidemia NOS
Hyperlipoproteinemia NOS
272.5 Lipoprotein deficiencies
Abetalipoproteinemia
Bassen-Kornzweig syndrome
High-density lipoid
deficiency
Hypoalphalipoproteinemia
Hypobetalipoproteinemia
(familial)
Barraquer-Simons disease
Progressive lipodystrophy
Use additional E
code to identify cause, if iatrogenic
Excludes: intestinal
lipodystrophy (040.2)
Chemically induced
lipidosis
Disease:
Anderson's
Fabry's
Gaucher's
I cell [mucolipidosis I]
lipoid storage NOS
Niemann-Pick
pseudo-Hurler's or mucolipidosis III
triglyceride storage, Type I or II
Wolman's or triglyceride
storage, Type III
Mucolipidosis II
Primary familial
xanthomatosis
Excludes: cerebral
lipidoses (330.1)
Tay-Sachs disease
(330.1)
272.8 Other disorders of lipoid metabolism
Hoffa's disease or
liposynovitis prepatellaris
Launois-Bensaude's lipomatosis
Lipoid dermatoarthritis
272.9 Unspecified disorder of lipoid metabolism
273.0 Polyclonal hypergammaglobulinemia
Hypergammaglobulinemic
purpura:
benign primary
Waldenström's
273.1 Monoclonal paraproteinemia
Benign monoclonal
hypergammaglobulinemia [BMH]
Monoclonal gammopathy:
NOS
associated with lymphoplasmacytic dyscrasias
benign
Paraproteinemia:
benign (familial)
secondary to malignant or inflammatory disease
Cryoglobulinemic:
purpura
vasculitis
Mixed cryoglobulinemia
Macroglobulinemia
(idiopathic) (primary)
Waldenström's
macroglobulinemia
275.1 Disorders of copper metabolism
Hepatolenticular
degeneration
Wilson's disease
275.2 Disorders of magnesium metabolism
Hypermagnesemia
Hypomagnesemia
Excludes: diabetes
insipidus (253.5)
familial periodic paralysis (359.3)
276.0 Hyperosmolality and/or hypernatremia
Sodium [Na] excess
Sodium [Na] overload
276.1 Hyposmolality and/or hyponatremia
Sodium [Na] deficiency
Dehydration
Depletion of volume of
plasma or extracellular fluid
Hypovolemia
Excludes: hypovolemic
shock:
postoperative (998.0)
traumatic (958.4)
Fluid retention
Excludes: ascites
(789.5)
localized edema (782.3)
Hyperkalemia
Potassium [K]:
excess
intoxication
overload
Hypokalemia
Potassium [K] deficiency
277.1 Disorders of porphyrin metabolism
Hematoporphyria
Hematoporphyrinuria
Hereditary coproporphyria
Porphyria
Porphyrinuria
Protocoproporphyria
Protoporphyria
Pyrroloporphyria
277.2 Other disorders of purine and pyrimidine metabolism
Hypoxanthine-guanine-phosphoribosyltransferase
deficiency [HG-PRT deficiency]
Lesch-Nyhan syndrome
Xanthinuria
Excludes: gout
(274.0-274.9)
orotic aciduric anemia (281.4)
Amyloidosis:
NOS
inherited systemic
nephropathic
neuropathic (Portuguese) (Swiss)
secondary
Benign paroxysmal
peritonitis
Familial Mediterranean
fever
Hereditary cardiac
amyloidosis
Gargoylism
Hunter's syndrome
Hurler's syndrome
Lipochondrodystrophy
Maroteaux-Lamy syndrome
Morquio-Brailsford disease
Osteochondrodystrophy
Sanfilippo's syndrome
Scheie's syndrome
277.8 Other specified disorders of metabolism
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
Carnitine deficiency due
to:
Hemodialysis
Valproic acid therapy
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
Carnitine
palmitoyltransferase deficiencies (CPT1, CPT2)
Glutaric aciduria type II
(type IIA, IIB, IIC)
Long chain 3-hydroxyacyl
CoA dehydrogenase deficiency (LCHAD)
Long chain/very long chain
acyl CoA dehydrogenase deficiency (LCAD, VLCAD)
Medium chain acyl CoA
dehydrogenase deficiency (MCAD)
Short chain acyl CoA
dehydrogenase deficiency (SCAD)
Excludes: primary
carnitine deficiency (277.81)
Adrenomyeloneuropathy
Neonatal
adrenoleukodystrophy
Rhizomelic
chrondrodysplasia punctata
X-linked
adrenoleukodystrophy
Zellweger syndrome
Excludes: infantile
Refsum disease (356.3)
277.87 Disorders of mitochondrial metabolism
Kearns-Sayre syndrome
Mitochondrial
Encephalopathy, Lactic Acidosis and Stroke-like episodes (MELAS syndrome)
Mitochondrial
Neurogastrointestinal Encephalopathy syndrome (MNGIE)
Myoclonus with Epilepsy and
with Ragged Red Fibers
(MERRF syndrome)
Neuropathy, Ataxia and
Retinitis Pigmentosa (NARP
syndrome)
Use additional
code for associated conditions
Excludes: disorders of pyruvate metabolism (271.8)
Leber's optic
atrophy (377.16)
Leigh's subacute
necrotizing encephalopathy (330.8)
Reye's syndrome
(331.81)
277.89 Other specified disorders of metabolism
Hand-Schüller-Christian
disease
Histiocytosis (acute)
(chronic)
Histiocytosis X (chronic)
Excludes: histiocytosis:
acute differentiated progressive (202.5)
X, acute (progressive)
(202.5)
277.9 Unspecified disorder of metabolism
Enzymopathy NOS
Anemia:
Addison's
Biermer's
congenital pernicious
Congenital intrinsic factor
[Castle's] deficiency
Excludes: combined
system disease without mention of anemia (266.2)
subacute degeneration of spinal cord without mention of anemia
(266.2)
Sickle-cell anemia
Excludes: sickle-cell
thalassemia (282.41-282.42)
sickle-cell trait (282.5)
282.60 Sickle-cell disease, unspecified
Sickle-cell anemia NOS
282.62 Hb-SS disease with crisis
Hb-SS disease with
vaso-occlusive pain
Sickle-cell crisis NOS
282.63 Sickle-cell/Hb-C disease without crisis
Hb-S/Hb-C disease without
crisis
282.64 Sickle-cell/HB-C disease with crisis
Hb-S/Hb-C disease with
crisis
Sickle-cell/Hb-C disease
with vaso-occlusive pain
Use additional
code for types of crisis, such as:
Acute chest
syndrome (517.3)
Splenic
sequestration (289.52)
Splenic sequestration (289.52)
286.0 Congenital factor VIII disorder
Antihemophilic globulin
[AHG] deficiency
Factor VIII (functional)
deficiency
Hemophilia:
NOS
A
classical
familial
hereditary
Subhemophilia
Excludes: factor
VIII deficiency with vascular defect (286.4)
286.1 Congenital factor IX disorder
Christmas disease
Deficiency:
factor IX (functional)
plasma thromboplastin component [PTC]
Hemophilia B
286.2 Congenital factor XI deficiency
Hemophilia C
Plasma thromboplastin
antecedent [PTA] deficiency
Rosenthal's disease
286.3 Congenital deficiency of other clotting factors
Congenital afibrinogenemia
Deficiency:
AC globulin
factor:
I [fibrinogen]
II [prothrombin]
V [labile]
VII [stable]
X [Stuart-Prower]
XII [Hageman]
XIII [fibrin stabilizing]
Laki-Lorand factor
proaccelerin
Disease:
Owren's
Stuart-Prower
Dysfibrinogenemia
(congenital)
Dysprothrombinemia
(constitutional)
Hypoproconvertinemia
Hypoprothrombinemia
(hereditary)
Parahemophilia
286.4 von Willebrand's disease
Angiohemophilia (A) (B)
Constitutional thrombopathy
Factor VIII deficiency with
vascular defect
Pseudohemophilia type B
Vascular hemophilia
von
Willebrand's (-Jürgens') disease
Excludes: factor
VIII deficiency:
NOS (286.0)
with functional defect (286.0)
hereditary capillary fragility (287.8)
286.5 Hemorrhagic disorder due to intrinsic circulating anticoagulants
Antithrombinemia
Antithromboplastinemia
Antithromboplastino-genemia
Hyperheparinemia
Increase in:
anti-VIIIa
anti-IXa
anti-Xa
anti-XIa
antithrombin
Secondary hemophilia
Systemic lupus
erythematosus [SLE] inhibitor
Afibrinogenemia, acquired
Consumption coagulopathy
Diffuse or disseminated
intravascular coagulation [DIC syndrome]
Fibrinolytic hemorrhage,
acquired
Hemorrhagic fibrinogenolysis
Pathologic fibrinolysis
Purpura:
fibrinolytic
fulminans
Excludes: that
complicating:
abortion (634-638 with .1, 639.1)
pregnancy or the puerperium (641.3, 666.3)
disseminated intravascular coagulation in newborn (776.2)
286.7 Acquired coagulation factor deficiency
Deficiency of coagulation
factor due to:
liver disease
vitamin K deficiency
Hypoprothrombinemia,
acquired
Excludes: vitamin
K deficiency of newborn (776.0)
Use additional
E-code to identify cause, if drug-induced
286.9 Other and unspecified coagulation defects
Defective coagulation NOS
Deficiency, coagulation
factor NOS
Delay, coagulation
Disorder:
coagulation
hemostasis
Excludes: abnormal
coagulation profile (790.92)
hemorrhagic disease of newborn (776.0)
that complicating:
abortion (634-638 with .1, 639.1)
pregnancy or the puerperium (641.3, 666.3)
INFLAMMATORY DISEASES OF THE CENTRAL NERVOUS SYSTEM (320-326)
Includes: arachnoiditis bacterial
leptomeningitis bacterial
meningitis bacterial
meningoencephalitis bacterial
meningomyelitis bacterial
pachymeningitis bacterial
Meningitis due to
Hemophilus influenzae [H. influenzae]
320.2 Streptococcal meningitis
320.3 Staphylococcal meningitis
320.7 Meningitis in other bacterial diseases classified elsewhere
Code first underlying
disease as:
actinomycosis (039.8)
listeriosis (027.0)
typhoid fever (002.0)
whooping cough (033.0-033.9)
Excludes: meningitis
(in):
epidemic (036.0)
gonococcal (098.82)
meningococcal (036.0)
salmonellosis (003.21)
syphilis:
NOS (094.2)
congenital (090.42)
meningovascular (094.2)
secondary (091.81)
tuberculosis (013.0)
320.8 Meningitis due to other specified bacteria
Gram-negative anaerobes
Bacteroides (fragilis)
320.82 Meningitis due to gram-negative bacteria, not elsewhere classified
Aerobacter aerogenes
Escherichia coli [E. coli]
Friedlander bacillus
Klebsiella pneumoniae
Proteus morganii
Pseudomonas
Excludes: gram-negative
anaerobes (320.81)
320.89 Meningitis due to other specified bacteria
Bacillus pyocyaneus
320.9 Meningitis due to unspecified bacterium
Meningitis:
bacterial NOS
purulent NOS
pyogenic NOS
suppurative NOS
Includes: arachnoiditis due to organisms other
than bacteria
leptomeningitis due to organisms other than bacteria
meningitis due to organisms other than bacteria
pachymeningitis due to organisms other than bacteria
Code first underlying disease
(117.5)
321.1 Meningitis in other fungal diseases
Code first underlying
disease (110.0-118)
Excludes: meningitis
in:
candidiasis (112.83)
coccidioidomycosis (114.2)
histoplasmosis (115.01, 115.11, 115.91)
321.2 Meningitis due to viruses not elsewhere classified
Code first underlying
disease, as:
meningitis due to arbovirus (060.0-066.9)
Excludes: meningitis
(due to):
abacterial (047.0-047.9)
adenovirus (049.1)
aseptic NOS (047.9)
Coxsackie (virus)
(047.0)
ECHO virus (047.1)
enterovirus (047.0-047.9)
herpes simplex virus (054.72)
herpes zoster virus (053.0)
lymphocytic choriomeningitis virus (049.0)
mumps (072.1)
viral NOS (047.9)
meningo-eruptive syndrome (047.1)
321.3 Meningitis due to trypanosomiasis
Code first underlying
disease (086.0-086.9)
321.4 Meningitis in sarcoidosis
Code first underlying
disease (135)
321.8 Meningitis due to other nonbacterial organisms classified elsewhere
Code first underlying
disease
Excludes: leptospiral
meningitis (100.81)
Includes: arachnoiditis with no organism
specified as cause
leptomeningitis with no organism specified as cause
meningitis with no organism specified as cause
pachymeningitis with no organism specified as cause
Meningitis with clear
cerebrospinal fluid
Includes: acute disseminated encephalomyelitis
meningoencephalitis, except bacterial
meningomyelitis, except bacterial
myelitis (acute):
ascending
transverse
Excludes: bacterial:
meningoencephalitis (320.0-320.9)
meningomyelitis (320.0-320.9)
323.0 Encephalitis in viral diseases classified elsewhere
Code first underlying
disease, as:
cat-scratch disease (078.3)
infectious mononucleosis (075)
ornithosis (073.7)
Excludes: encephalitis
(in):
arthropod-borne viral (062.0-064)
herpes simplex (054.3)
mumps (072.2)
poliomyelitis (045.0-045.9)
rubella (056.01)
slow virus infections of central nervous system
(046.0-046.9)
other viral diseases of central nervous system
(049.8-049.9)
viral NOS (049.9)
323.1 Encephalitis in rickettsial diseases classified elsewhere
Code first underlying
disease (080-083.9)
323.2 Encephalitis in protozoal diseases classified elsewhere
Code first underlying
disease, as:
malaria (084.0-084.9)
trypanosomiasis (086.0-086.9)
323.4 Other encephalitis due to infection classified elsewhere
Code first underlying
disease
Excludes: encephalitis
(in):
meningococcal (036.1)
syphilis:
NOS (094.81)
congenital (090.41)
toxoplasmosis (130.0)
tuberculosis (013.6)
meningoencephalitis due to free-living ameba [Naegleria] (136.2)
323.5 Encephalitis following immunization procedures
Encephalitis
postimmunization or postvaccinal
Encephalomyelitis
postimmunization or postvaccinal
Use additional E
code to identify vaccine
323.6 Postinfectious encephalitis
Code first underlying
disease
Excludes: encephalitis:
postchickenpox (052.0)
postmeasles (055.0)
Code first underlying cause,
as:
carbon tetrachloride (982.1)
hydroxyquinoline derivatives (961.3)
lead (984.0-984.9)
mercury (985.0)
thallium (985.8)
323.8 Other causes of encephalitis
323.9 Unspecified cause of encephalitis
Abscess (embolic):
cerebellar
cerebral
Abscess (embolic) of brain
[any part]:
epidural
extradural
otogenic
subdural
Excludes: tuberculous
(013.3)
Abscess (embolic) of spinal
cord [any part]:
epidural
extradural
subdural
Excludes: tuberculous
(013.5)
Extradural or subdural
abscess NOS
Embolism of cavernous,
lateral, or other intracranial or unspecified intracranial venous sinus
Endophlebitis of cavernous,
lateral, or other intracranial or unspecified intracranial venous sinus
Phlebitis, septic or
suppurative of cavernous, lateral, or other intracranial or unspecified
intracranial venous sinus
Thrombophlebitis of
cavernous, lateral, or other intracranial or unspecified intracranial venous
sinus
Thrombosis of cavernous,
lateral, or other intracranial or unspecified intracranial venous sinus
Excludes: that
specified as:
complicating pregnancy, childbirth, or the puerperium (671.5)
of nonpyogenic origin (437.6)
Note: This category is to be used to indicate
conditions whose primary classification is to 320-325 [excluding 320.7,
321.0-321.8, 323.0-323.4, 323.6-323.7] as the cause of late effects,
themselves classifiable elsewhere. The "late effects" include
conditions specified as such, or as sequelae, which may occur at any time after
the resolution of the causal condition.
Use additional code to
identify condition, as:
hydrocephalus (331.4)
paralysis (342.0-342.9, 344.0-344.9)
HEREDITARY AND DEGENERATIVE DISEASES OF THE CENTRAL NERVOUS SYSTEM (330-337)
Excludes: hepatolenticular degeneration (275.1)
multiple sclerosis (340)
other demyelinating diseases of central nervous system
(341.0-341.9)
Use additional code to
identify associated mental retardation
Krabbe's disease
Leukodystrophy:
NOS
globoid cell
metachromatic
sudanophilic
Pelizaeus-Merzbacher
disease
Sulfatide lipidosis
Amaurotic (familial) idiocy
Disease:
Batten
Jansky-Bielschowsky
Kufs'
Spielmeyer-Vogt
Tay-Sachs
Gangliosidosis
330.2 Cerebral degeneration in generalized lipidoses
Code first underlying
disease, as:
Fabry's disease
(272.7)
Gaucher's disease
(272.7)
Niemann-Pick disease
(272.7)
sphingolipidosis (272.7)
330.3 Cerebral degeneration of childhood in other diseases classified elsewhere
Code first underlying
disease, as:
Hunter's disease
(277.5)
mucopolysaccharidosis (277.5)
330.8 Other specified cerebral degenerations in childhood
Alpers' disease or
gray-matter degeneration
Infantile necrotizing
encephalomyelopathy
Leigh's disease
Subacute necrotizing
encephalopathy or encephalomyelopathy
330.9 Unspecified cerebral degeneration in childhood
Use additional
code for associated behavioral disturbances (294.10-294.11)
331.19 Other frontotemporal dementia
Frontal dementia
331.2 Senile degeneration of brain
Excludes: senility
NOS (797)
331.3 Communicating hydrocephalus
Excludes: congenital
hydrocephalus (741.0, 742.3)
331.4 Obstructive hydrocephalus
Acquired hydrocephalus NOS
Excludes: congenital
hydrocephalus (741.0, 742.3)
331.7 Cerebral degeneration in diseases classified elsewhere
Code first underlying
disease, as:
alcoholism (303.0-303.9)
beriberi (265.0)
cerebrovascular disease (430-438)
congenital hydrocephalus (741.0, 742.3)
neoplastic disease (140.0-239.9)
myxedema (244.0-244.9)
vitamin B12 deficiency (266.2)
Excludes: cerebral
degeneration in:
Jakob-Creutzfeldt
disease (046.1)
progressive multifocal leukoencephalopathy (046.3)
subacute spongiform encephalopathy (046.1)
331.8 Other cerebral degeneration
331.82 Dementia with Lewy bodies
Dementia with Parkinsonism
Lewy body dementia
Lewy body disease
Use additional
code for associated behavioral disturbances (294.10-294.11)
Cerebral ataxia
331.9 Cerebral degeneration, unspecified
Excludes: dementia
with Parkinsonism (331.82)
Parkinsonism or Parkinson's
disease:
NOS
idiopathic
primary
Parkinsonism due to drugs
Use additional E
code to identify drug, if drug-induced
Excludes: Parkinsonism
(in):
Huntington's
disease (333.4)
progressive supranuclear palsy (333.0)
Shy-Drager
syndrome (333.0)
syphilitic (094.82)
Includes: other forms of extrapyramidal, basal
ganglia, or striatopallidal disease
Excludes: abnormal
movements of head NOS (781.0)
333.0 Other degenerative diseases of the basal ganglia
Atrophy or degeneration:
olivopontocerebellar [Déjérine-Thomas syndrome]
pigmentary pallidal [Hallervorden-Spatz disease] striatonigral
Parkinsonian syndrome
associated with:
idiopathic orthostatic hypotension
symptomatic orthostatic hypotension
Progressive supranuclear
ophthalmoplegia
Shy-Drager syndrome
333.1 Essential and other specified forms of tremor
Benign essential tremor
Familial tremor
Use additional E
code to identify drug, if drug-induced
Excludes: tremor
NOS (781.0)
Familial essential
myoclonus
Progressive myoclonic
epilepsy
Unverricht-Lundborg disease
Use additional E
code to identify drug, if drug-induced
Excludes: Gilles
de la Tourette's syndrome (307.23)
habit spasm (307.22)
tic NOS (307.20)
Use additional E
code to identify drug, if drug-induced
Hemiballism(us)
Paroxysmal choreo-athetosis
Excludes: Sydenham's
or rheumatic chorea (392.0-392.9)
Use additional E
code to identify drug, if drug-induced
333.6 Idiopathic torsion dystonia
Dystonia:
deformans progressiva
musculorum deformans
(Schwalbe-)
Ziehen-Oppenheim disease
333.7 Symptomatic torsion dystonia
Athetoid cerebral palsy
[Vogt's disease]
Double athetosis (syndrome)
Use additional E
code to identify drug, if drug-induced
333.8 Fragments of torsion dystonia
Use additional E
code to identify drug, if drug-induced
Excludes: torticollis:
NOS (723.5)
hysterical (300.11)
psychogenic (306.0)
Excludes: psychogenic
(300.89)
333.9 Other and unspecified extrapyramidal diseases and abnormal movement disorders
333.90 Unspecified extrapyramidal disease and abnormal movement disorder
333.92 Neuroleptic malignant syndrome
Use additional E
to identify drug
333.93 Benign shuddering attacks
Restless legs
Excludes: olivopontocerebellar
degeneration (333.0)
peroneal muscular atrophy (356.1)
334.1 Hereditary spastic paraplegia
334.2 Primary cerebellar degeneration
Cerebellar ataxia:
Marie's
Sanger-Brown
Dyssynergia cerebellaris
myoclonica
Primary cerebellar
degeneration:
NOS
hereditary
sporadic
Cerebellar ataxia NOS
Use additional E
code to identify drug, if drug-induced
334.4 Cerebellar ataxia in diseases classified elsewhere
Code first underlying
disease, as:
alcoholism (303.0-303.9)
myxedema (244.0-244.9)
neoplastic disease (140.0-239.9)
334.8 Other spinocerebellar diseases
Ataxia-telangiectasia
[Louis-Bar syndrome]
Corticostriatal-spinal
degeneration
334.9 Spinocerebellar disease, unspecified
335.0 Werdnig-Hoffmann disease
Infantile spinal muscular
atrophy
Progressive muscular
atrophy of infancy
335.10 Spinal muscular atrophy, unspecified
335.11 Kugelberg-Welander disease
Spinal muscular atrophy:
familial
juvenile
Adult spinal muscular
atrophy
335.20 Amyotrophic lateral sclerosis
Motor neuron disease
(bulbar) (mixed type)
335.21 Progressive muscular atrophy
Duchenne-Aran muscular
atrophy
Progressive muscular
atrophy (pure)
335.22 Progressive bulbar palsy
335.24 Primary lateral sclerosis
335.8 Other anterior horn cell diseases
335.9 Anterior horn cell disease, unspecified
336.0 Syringomyelia and syringobulbia
Acute infarction of spinal
cord (embolic) (nonembolic)
Arterial thrombosis of
spinal cord
Edema of spinal cord
Hematomyelia
Subacute necrotic myelopathy
336.2 Subacute combined degeneration of spinal cord in diseases classified elsewhere
Code first underlying
disease, as:
pernicious anemia (281.0)
other vitamin B12 deficiency anemia (281.1)
vitamin B12 deficiency (266.2)
336.3 Myelopathy in other diseases classified elsewhere
Code first underlying
disease, as:
myelopathy in neoplastic disease (140.0-239.9)
Excludes: myelopathy
in:
intervertebral disc disorder (722.70-722.73)
spondylosis (721.1, 721.41-721.42, 721.91)
Myelopathy:
drug-induced
radiation-induced
Use additional E
code to identify cause
336.9 Unspecified disease of spinal cord
Cord compression NOS
Myelopathy NOS
Excludes: myelitis
(323.0-323.9)
spinal (canal) stenosis (723.0, 724.00-724.09)
Includes: disorders of peripheral autonomic,
sympathetic, parasympathetic, or vegetative system
Excludes: familial
dysautonomia [Riley-Day syndrome] (742.8)
337.0 Idiopathic peripheral autonomic neuropathy
Carotid sinus syncope or
syndrome
Cervical sympathetic
dystrophy or paralysis
337.1 Peripheral autonomic neuropathy in disorders classified elsewhere
Code first underlying
disease, as:
amyloidosis (277.3)
diabetes (250.6)
337.2 Reflex sympathetic dystrophy
337.20 Reflex sympathetic dystrophy, unspecified
337.21 Reflex sympathetic dystrophy of the upper limb
337.22 Reflex sympathetic dystrophy of the lower limb
337.29 Reflex sympathetic dystrophy of other specified site
Use additional code to
identify the cause, such as:
decubitus ulcer (707.00-707.09)
fecal impaction (560.39)
urinary tract infection (599.0)
337.9 Unspecified disorder of autonomic nervous system
OTHER DISORDERS OF THE CENTRAL NERVOUS SYSTEM (340-349)
Disseminated or multiple
sclerosis:
NOS
brain stem
cord
generalized
Balo's concentric sclerosis
Encephalitis periaxialis:
concentrica [Balo's]
diffusa [Schilder's]
341.8 Other demyelinating diseases of central nervous system
Central demyelination of
corpus callosum
Central pontine myelinosis
Marchiafava (-Bignami)
disease
341.9 Demyelinating disease of central nervous system, unspecified
Note: This category is to be used when hemiplegia
(complete) (incomplete) is reported without further specification, or is stated
to be old or long-standing but of unspecified cause. The category is also for use in multiple
coding to identify these types of hemiplegia resulting from any cause.
Excludes: congenital
(343.1)
hemiplegia due to late effect of cerebrovascular accident
(438.20-438.22)
infantile NOS (343.4)
The following fifth-digits are
for use with codes 342.0-342.9
0 affecting unspecified side
1 affecting dominant side
2 affecting nondominant side
342.8 Other specified hemiplegia
Includes: cerebral:
palsy NOS
spastic infantile paralysis
congenital spastic paralysis (cerebral)
Little's disease
paralysis (spastic) due to birth injury:
intracranial
spinal
Excludes: hereditary
cerebral paralysis, such as:
hereditary spastic paraplegia (334.1)
Vogt's disease
(333.7)
spastic paralysis specified as noncongenital or noninfantile
(344.0-344.9)
Congenital diplegia
Congenital paraplegia
Congenital hemiplegia
Excludes: infantile
hemiplegia NOS (343.4)
Tetraplegic
Infantile hemiplegia
(postnatal) NOS
343.8 Other specified infantile cerebral palsy
343.9 Infantile cerebral palsy, unspecified
Cerebral palsy NOS
Note: This category is to be used when the listed
conditions are reported without further specification or are stated to be old
or long-standing but of unspecified cause. The category is also for use in
multiple coding to identify these conditions resulting from any cause.
Includes: paralysis (complete) (incomplete),
except as classifiable to 342 and 343
Excludes: congenital
or infantile cerebral palsy (343.0-343.9)
hemiplegia (342.0-342.9)
congenital or infantile (343.1, 343.4)
344.0 Quadriplegia and quadriparesis
344.00 Quadriplegia, unspecified
Paralysis of both lower
limbs
Paraplegia (lower)
Diplegia (upper)
Paralysis of both upper
limbs
344.3 Monoplegia of lower limb
Paralysis of lower limb
Excludes: monoplegia
of lower limb due to late effect of cerebrovascular accident (438.40-438.42)
344.30 Affecting unspecified side
344.31 Affecting dominant side
344.32 Affecting nondominant side
344.4 Monoplegia of upper limb
Paralysis of upper limb
Excludes: monoplegia
of upper limb due to late effect of cerebrovascular accident (438.30-438.32)
344.40 Affecting unspecified side
344.41 Affecting dominant side
344.42 Affecting nondominant side
344.60 Without mention of neurogenic bladder
344.61 With neurogenic bladder
Acontractile bladder
Autonomic hyperreflexia of
bladder
Cord bladder
Detrusor hyperreflexia
344.8 Other specified paralytic syndromes
344.89 Other specified paralytic syndrome
The following fifth-digit
subclassification is for use with categories 345.0, .1, .4-.9:
0 without mention of intractable epilepsy
1 with intractable epilepsy
Excludes: progressive
myoclonic epilepsy (333.2)
345.0 Generalized nonconvulsive epilepsy
Absences:
atonic
typical
Minor epilepsy
Petit mal
Pykno-epilepsy
Seizures:
akinetic
atonic
345.1 Generalized convulsive epilepsy
Epileptic seizures:
clonic
myoclonic
tonic
tonic-clonic
Grand mal
Major epilepsy
Excludes: convulsions:
NOS (780.3)
infantile (780.3)
newborn (779.0)
infantile spasms (345.6)
Epileptic absence status
Status epilepticus NOS
Excludes: epilepsia
partialis continua (345.7) status:
psychomotor (345.7)
temporal lobe (345.7)
345.4 Partial epilepsy, with impairment of consciousness
Epilepsy:
limbic system
partial:
secondarily generalized
with memory and ideational disturbances
psychomotor
psychosensory
temporal lobe
Epileptic automatism
345.5 Partial epilepsy, without mention of impairment of consciousness
Epilepsy:
Bravais-Jacksonian NOS
focal (motor) NOS
Jacksonian NOS
motor partial
partial NOS
sensory-induced
somatomotor
somatosensory
visceral
visual
Hypsarrhythmia
Lightning spasms
Salaam attacks
Excludes: salaam
tic (781.0)
345.7 Epilepsia partialis continua
Kojevnikov's epilepsy
Epilepsy:
cursive [running]
gelastic
Epileptic convulsions,
fits, or seizures NOS
Excludes: convulsive
seizure or fit NOS (780.3)
The following fifth-digit
subclassification is for use with category 346:
0 without mention of intractable migraine
1 with intractable migraine, so stated
Migraine preceded or
accompanied by transient focal neurological phenomena
Migraine with aura
Atypical migraine
Sick headache
Cluster headache
Histamine cephalgia
Horton's neuralgia
Migraine:
abdominal
basilar
lower half
retinal
Neuralgia:
ciliary
migrainous
Migraine:
hemiplegic
ophthalmoplegic
Narcolepsy NOS
347.1 Narcolepsy in conditions classified elsewhere
Code first underlying
condition
Arachnoid cyst
Porencephalic cyst
Porencephaly, acquired
Pseudoporencephaly
Excludes: that
occurring in:
abortion (634-638 with .7, 639.8)
ectopic or molar pregnancy (639.8)
labor or delivery (668.2, 669.4)
that of newborn (767.0, 768.0-768.9, 772.1-772.2)
Use additional E
code to identify cause
348.2 Benign intracranial hypertension
Pseudotumor cerebri
Excludes: hypertensive
encephalopathy (437.2)
348.3 Encephalopathy, not elsewhere classified
348.30 Encephalopathy, unspecified
348.31 Metabolic encephalopathy
Septic encephalopathy
Excludes: encephalopathy:
alcoholic (291.2)
hepatic (572.2)
hypertensive (437.2)
toxic (349.82)
Compression brain (stem)
Herniation brain (stem)
Posterior fossa compression
syndrome
348.8 Other conditions of brain
Cerebral:
calcification
fungus
348.9 Unspecified condition of brain
349.0 Reaction to spinal or lumbar puncture
Headache following lumbar
puncture
349.1 Nervous system complications from surgically implanted device
Excludes: immediate
postoperative complications (997.00-997.09)
mechanical complications of nervous system device (996.2)
349.2 Disorders of meninges, not elsewhere classified
Adhesions, meningeal
(cerebral) (spinal)
Cyst, spinal meninges
Meningocele, acquired
Pseudomeningocele, acquired
349.8 Other specified disorders of nervous system
349.81 Cerebrospinal fluid rhinorrhea
Excludes: cerebrospinal
fluid otorrhea (388.61)
Use additional E
code to identify cause
349.9 Unspecified disorders of nervous system
Disorder of nervous system
(central) NOS
DISORDERS OF THE PERIPHERAL NERVOUS SYSTEM (350-359)
Excludes: diseases of:
acoustic [8th] nerve (388.5)
oculomotor [3rd, 4th, 6th] nerves (378.0-378.9)
optic [2nd] nerve (377.0-377.9)
peripheral autonomic nerves (337.0-337.9)
neuralgia NOS or "rheumatic" (729.2)
neuritis NOS or "rheumatic" (729.2)
radiculitis NOS or "rheumatic" (729.2)
peripheral neuritis in pregnancy (646.4)
Includes: disorders of 5th cranial nerve
Tic douloureux
Trifacial neuralgia
Trigeminal neuralgia NOS
Excludes: postherpetic
(053.12)
350.8 Other specified trigeminal nerve disorders
350.9 Trigeminal nerve disorder, unspecified
Includes: disorders of 7th cranial nerve
Excludes: that
in newborn (767.5)
Facial palsy
Geniculate ganglionitis NOS
Excludes: herpetic
(053.11)
351.8 Other facial nerve disorders
Facial myokymia
Melkersson's syndrome
351.9 Facial nerve disorder, unspecified
352.0 Disorders of olfactory [1st] nerve
352.1 Glossopharyngeal neuralgia
352.2 Other disorders of glossopharyngeal [9th] nerve
352.3 Disorders of pneumogastric [10th] nerve
Disorders of vagal nerve
Excludes: paralysis
of vocal cords or larynx (478.30-478.34)
352.4 Disorders of accessory [11th] nerve
352.5 Disorders of hypoglossal [12th] nerve
352.6 Multiple cranial nerve palsies
Collet-Sicard syndrome
Polyneuritis cranialis
352.9 Unspecified disorder of cranial nerves
Excludes: conditions
due to:
intervertebral disc disorders (722.0-722.9)
spondylosis (720.0-721.9)
vertebrogenic disorders (723.0-724.9)
Cervical rib syndrome
Costoclavicular syndrome
Scalenus anticus syndrome
Thoracic outlet syndrome
Excludes: brachial
neuritis or radiculitis NOS (723.4)
that in newborn (767.6)
353.1 Lumbosacral plexus lesions
353.2 Cervical root lesions, not elsewhere classified
353.3 Thoracic root lesions, not elsewhere classified
353.4 Lumbosacral root lesions, not elsewhere classified
Parsonage-Aldren-Turner
syndrome
353.8 Other nerve root and plexus disorders
353.9 Unspecified nerve root and plexus disorder
Median nerve entrapment
Partial thenar atrophy
354.1 Other lesion of median nerve
Median nerve neuritis
Cubital tunnel syndrome
Tardy ulnar nerve palsy
Acute radial nerve palsy
Excludes: causalgia:
NOS (355.9)
lower limb (355.71)
Combinations of single
conditions classifiable to 354 or 355
354.8 Other mononeuritis of upper limb
354.9 Mononeuritis of upper limb, unspecified
Excludes: sciatica
NOS (724.3)
Lateral cutaneous femoral
nerve of thigh compression or syndrome
355.2 Other lesion of femoral nerve
355.3 Lesion of lateral popliteal nerve
Lesion of common peroneal
nerve
355.4 Lesion of medial popliteal nerve
Morton's metatarsalgia,
neuralgia, or neuroma
355.7 Other mononeuritis of lower limb
355.71 Causalgia of lower limb
Excludes: causalgia:
NOS (355.9)
upper limb (354.4)
355.79 Other mononeuritis of lower limb
355.8 Mononeuritis of lower limb, unspecified
355.9 Mononeuritis of unspecified site
Causalgia NOS
Excludes: causalgia:
lower limb (355.71)
upper limb (354.4)
356.0 Hereditary peripheral neuropathy
Déjérine-Sottas disease
356.1 Peroneal muscular atrophy
Charcot-Marie-Tooth disease
Neuropathic muscular
atrophy
356.2 Hereditary sensory neuropathy
Heredopathia atactica
polyneuritiformis
356.4 Idiopathic progressive polyneuropathy
356.8 Other specified idiopathic peripheral neuropathy
Supranuclear paralysis
357.0 Acute infective polyneuritis
Guillain-Barre syndrome
Postinfectious polyneuritis
357.1 Polyneuropathy in collagen vascular disease
Code first underlying
disease, as:
disseminated lupus erythematosus (710.0)
polyarteritis nodosa (446.0)
rheumatoid arthritis (714.0)
357.2 Polyneuropathy in diabetes
Code first underlying
disease (250.6)
357.3 Polyneuropathy in malignant disease
Code first underlying
disease (140.0-208.9)
357.4 Polyneuropathy in other diseases classified elsewhere
Code first underlying
disease, as:
amyloidosis (277.3)
beriberi (265.0)
deficiency of B vitamins (266.0-266.9)
diphtheria (032.0-032.9)
hypoglycemia (251.2)
pellagra (265.2)
porphyria (277.1)
sarcoidosis (135)
uremia (585)
Excludes: polyneuropathy
in:
herpes zoster (053.13)
mumps (072.72)
357.5 Alcoholic polyneuropathy
357.6 Polyneuropathy due to drugs
Use additional E
code to identify drug
357.7 Polyneuropathy due to other toxic agents
Use additional E
code to identify toxic agent
357.81 Chronic inflammatory demyelinating polyneuritis
357.82 Critical illness polyneuropathy
Acute motor neuropathy
357.89 Other inflammatory and toxic neuropathy
358.00 Myasthenia gravis without (acute) exacerbation
358.01 Myasthenia gravis with (acute) exacerbation
Myasthenia gravis in crisis
358.1 Myasthenic syndromes in diseases classified elsewhere
Amyotrophy from stated
cause classified elsewhere
Eaton-Lambert syndrome from
stated cause classified elsewhere
Code first underlying
disease, as:
botulism (005.1)
diabetes mellitus (250.6)
hypothyroidism (244.0-244.9)
malignant neoplasm (140.0-208.9)
pernicious anemia (281.0)
thyrotoxicosis (242.0-242.9)
358.2 Toxic myoneural disorders
Use additional E
code to identify toxic agent
358.8 Other specified myoneural disorders
358.9 Myoneural disorders, unspecified
Excludes: idiopathic
polymyositis (710.4)
359.0 Congenital hereditary muscular dystrophy
Benign congenital myopathy
Central core disease
Centronuclear myopathy
Myotubular myopathy
Nemaline body disease
Excludes: arthrogryposis
multiplex congenita (754.89)
359.1 Hereditary progressive muscular dystrophy
Muscular dystrophy:
NOS
distal
Duchenne
Erb's
fascioscapulohumeral
Gower's
Landouzy-Déjérine
limb-girdle
ocular
oculopharyngeal
Dystrophia myotonica
Eulenburg's disease
Myotonia congenita
Paramyotonia congenita
Steinert's disease
Thomsen's disease
359.3 Familial periodic paralysis
Hypokalemic familial
periodic paralysis
Use additional E
code to identify toxic agent
359.5 Myopathy in endocrine diseases classified elsewhere
Code first underlying
disease, as:
Addison's disease
(255.4)
Cushing's syndrome
(255.0)
hypopituitarism (253.2)
myxedema (244.0-244.9)
thyrotoxicosis (242.0-242.9)
359.6 Symptomatic inflammatory myopathy in diseases classified elsewhere
Code first underlying
disease, as:
amyloidosis (277.3)
disseminated lupus erythematosus (710.0)
malignant neoplasm (140.0-208.9)
polyarteritis nodosa (446.0)
rheumatoid arthritis (714.0)
sarcoidosis (135)
scleroderma (710.1)
Sjögren's disease
(710.2)
359.81 Critical illness myopathy
Acute necrotizing myopathy
Acute quadriplegic myopathy
Intensive care (ICU)
myopathy
Myopathy of critical
illness
362.3 Retinal vascular occlusion
362.30 Retinal vascular occlusion, unspecified
362.31 Central retinal artery occlusion
362.32 Arterial branch occlusion
362.33 Partial arterial occlusion
Hollenhorst plaque
Retinal microembolism
362.34 Transient arterial occlusion
Amaurosis fugax
362.35 Central retinal vein occlusion
Excludes: electrophysiological
disturbances (794.11-794.14)
Suppression amblyopia
368.1 Subjective visual disturbances
368.10 Subjective visual disturbance, unspecified
Concentric fading
Scintillating scotoma
Asthenopia
Eye strain
Photophobia
368.14 Visual distortions of shape and size
Macropsia
Metamorphopsia
Micropsia
368.15 Other visual distortions and entoptic phenomena
Photopsia
Refractive:
diplopia
polyopia
Visual halos
368.16 Psychophysical visual disturbances
Visual:
agnosia
disorientation syndrome
hallucinations
Double vision
368.3 Other disorders of binocular vision
368.30 Binocular vision disorder, unspecified
368.31 Suppression of binocular vision
368.32 Simultaneous visual perception without fusion
368.33 Fusion with defective stereopsis
368.34 Abnormal retinal correspondence
368.40 Visual field defect, unspecified
368.41 Scotoma involving central area
Scotoma:
central
centrocecal
paracentral
368.42 Scotoma of blind spot area
Enlarged:
angioscotoma
blind spot
Paracecal scotoma
368.43 Sector or arcuate defects
Scotoma:
arcuate
Bjerrum
Seidel
368.44 Other localized visual field defect
Scotoma:
NOS
ring
Visual field defect:
nasal step
peripheral
368.45 Generalized contraction or constriction
368.46 Homonymous bilateral field defects
Hemianopsia (altitudinal)
(homonymous)
Quadrant anopia
368.47 Heteronymous bilateral field defects
Hemianopsia:
binasal
bitemporal
368.5 Color vision deficiencies
Color blindness
Protanomaly
Protanopia
Deuteranomaly
Deuteranopia
Tritanomaly
Tritanopia
Monochromatism (cone) (rod)
368.55 Acquired color vision deficiencies
368.59 Other color vision deficiencies
376.1 Chronic inflammatory disorders of orbit
376.10 Chronic inflammation of orbit, unspecified
Pseudotumor (inflammatory)
of orbit
Code first underlying thyroid disorder (242.0-242.9)
376.21 Thyrotoxic exophthalmos
376.22 Exophthalmic ophthalmoplegia
376.3 Other exophthalmic conditions
376.30 Exophthalmos, unspecified
376.33 Orbital edema or congestion
376.34 Intermittent exophthalmos
376.36 Lateral displacement of globe
377.00 Papilledema, unspecified
377.01 Papilledema associated with increased intracranial pressure
377.02 Papilledema associated with decreased ocular pressure
377.03 Papilledema associated with retinal disorder
377.04 Foster-Kennedy syndrome
377.10 Optic atrophy, unspecified
Excludes: neurosyphilitic
optic atrophy (094.84)
377.12 Postinflammatory optic atrophy
377.13 Optic atrophy associated with retinal dystrophies
377.14 Glaucomatous atrophy [cupping] of optic disc
Temporal pallor of optic
disc
377.16 Hereditary optic atrophy
Optic atrophy:
dominant hereditary
Leber's
377.2 Other disorders of optic disc
377.22 Crater-like holes of optic disc
Excludes: meningococcal
optic neuritis (036.81)
377.30 Optic neuritis, unspecified
377.32 Retrobulbar neuritis (acute)
Excludes: syphilitic
retrobulbar neuritis (094.85)
377.33 Nutritional optic neuropathy
Toxic amblyopia
Excludes: ischemic
optic neuropathy (377.41)
377.4 Other disorders of optic nerve
377.41 Ischemic optic neuropathy
377.42 Hemorrhage in optic nerve sheaths
377.49 Other Compression of optic nerve
377.5 Disorders of optic chiasm
377.51 Associated with pituitary neoplasms and disorders
377.52 Associated with other neoplasms
377.53 Associated with vascular disorders
377.54 Associated with inflammatory disorders
377.6 Disorders of other visual pathways
377.61 Associated with neoplasms
377.62 Associated with vascular disorders
377.63 Associated with inflammatory disorders
377.7 Disorders of visual cortex
Excludes: visual:
agnosia (368.16)
hallucinations (368.16)
halos (368.15)
377.71 Associated with neoplasms
377.72 Associated with vascular disorders
377.73 Associated with inflammatory disorders
377.9 Unspecified disorder of optic nerve and visual pathways
Excludes: nystagmus
and other irregular eye movements (379.50-379.59)
Convergent concomitant
strabismus
Excludes: intermittent
esotropia (378.20-378.22)
378.02 Monocular esotropia with A pattern
378.03 Monocular esotropia with V pattern
378.04 Monocular esotropia with other noncomitancies
Monocular esotropia with X
or Y pattern
378.06 Alternating esotropia with A pattern
378.07 Alternating esotropia with V pattern
378.08 Alternating esotropia with other noncomitancies
Alternating esotropia with
X or Y pattern
Divergent concomitant
strabismus
Excludes: intermittent
exotropia (378.20, 378.23-378.24)
378.12 Monocular exotropia with A pattern
378.13 Monocular exotropia with V pattern
378.14 Monocular exotropia with other noncomitancies
Monocular exotropia with X
or Y pattern
378.16 Alternating exotropia with A pattern
378.17 Alternating exotropia with V pattern
378.18 Alternating exotropia with other noncomitancies
Alternating exotropia with
X or Y pattern
378.2 Intermittent heterotropia
Excludes: vertical
heterotropia (intermittent) (378.31)
378.20 Intermittent heterotropia, unspecified
Intermittent:
esotropia NOS
exotropia NOS
378.21 Intermittent esotropia, monocular
378.22 Intermittent esotropia, alternating
378.23 Intermittent exotropia, monocular
378.24 Intermittent exotropia, alternating
378.3 Other and unspecified heterotropia
378.30 Heterotropia, unspecified
Vertical heterotropia
(constant) (intermittent)
Microtropia
378.35 Accommodative component in esotropia
378.40 Heterophoria, unspecified
378.45 Alternating hyperphoria
378.50 Paralytic strabismus, unspecified
378.51 Third or oculomotor nerve palsy, partial
378.52 Third or oculomotor nerve palsy, total
378.53 Fourth or trochlear nerve palsy
378.54 Sixth or abducens nerve palsy
378.55 External ophthalmoplegia
378.60 Mechanical strabismus, unspecified
378.61 Brown's (tendon) sheath syndrome
378.62 Mechanical strabismus from other musculofascial disorders
378.63 Limited duction associated with other conditions
378.7 Other specified strabismus
378.72 Progressive external ophthalmoplegia
378.73 Strabismus in other neuromuscular disorders
378.8 Other disorders of binocular eye movements
Excludes: nystagmus
(379.50-379.56)
378.81 Palsy of conjugate gaze
378.82 Spasm of conjugate gaze
378.83 Convergence insufficiency or palsy
378.84 Convergence excess or spasm
378.85 Anomalies of divergence
378.86 Internuclear ophthalmoplegia
378.87 Other dissociated deviation of eye movements
Skew deviation
378.9 Unspecified disorder of eye movements
Ophthalmoplegia NOS
Strabismus NOS
379.4 Anomalies of pupillary function
379.40 Abnormal pupillary function, unspecified
379.42 Miosis (persistent), not due to miotics
379.43 Mydriasis (persistent), not due to mydriatics
379.45 Argyll Robertson pupil, atypical
Argyll Robertson phenomenon
or pupil, nonsyphilitic
Excludes: Argyll
Robertson pupil (syphilitic) (094.89)
379.46 Tonic pupillary reaction
Adie's pupil or syndrome
Hippus
Pupillary paralysis
379.5 Nystagmus and other irregular eye movements
379.53 Visual deprivation nystagmus
379.54 Nystagmus associated with disorders of the vestibular system
379.56 Other forms of nystagmus
379.57 Deficiencies of saccadic eye movements
Abnormal optokinetic
response
379.58 Deficiencies of smooth pursuit movements
379.59 Other irregularities of eye movements
Opsoclonus
379.8 Other specified disorders of eye and adnexa
379.9 Unspecified disorder of eye and adnexa
379.90 Disorder of eye, unspecified
379.92 Swelling or mass of eye
379.93 Redness or discharge of eye
379.99 Other ill-defined disorders of eye
Excludes: blurred
vision NOS (368.8)
DISEASES OF THE EAR AND MASTOID PROCESS (380-389)
Excludes: vertigo
NOS (780.4)
Endolymphatic hydrops
Lermoyez's syndrome
Méniére's syndrome or
vertigo
386.00 Méniére's disease, unspecified
Méniére's disease (active)
386.01 Active Méniére's disease, cochleovestibular
386.02 Active Méniére's disease, cochlear
386.03 Active Méniére's disease, vestibular
386.04 Inactive Méniére's disease
Méniére's disease in
remission
386.1 Other and unspecified peripheral vertigo
Excludes: epidemic
vertigo (078.81)
386.10 Peripheral vertigo, unspecified
386.11 Benign paroxysmal positional vertigo
Benign paroxysmal
positional nystagmus
Acute (and recurrent)
peripheral vestibulopathy
Aural vertigo
Otogenic vertigo
386.2 Vertigo of central origin
Central positional
nystagmus
Malignant positional
vertigo
386.30 Labyrinthitis, unspecified
Diffuse labyrinthitis
386.32 Circumscribed labyrinthitis
Focal labyrinthitis
386.33 Suppurative labyrinthitis
Purulent labyrinthitis
386.40 Labyrinthine fistula, unspecified
386.43 Semicircular canal fistula
386.48 Labyrinthine fistula of combined sites
386.5 Labyrinthine dysfunction
386.50 Labyrinthine dysfunction, unspecified
386.51 Hyperactive labyrinth, unilateral
386.52 Hyperactive labyrinth, bilateral
386.53 Hypoactive labyrinth, unilateral
386.54 Hypoactive labyrinth, bilateral
386.55 Loss of labyrinthine reactivity, unilateral
386.56 Loss of labyrinthine reactivity, bilateral
386.58 Other forms and combinations
386.8 Other disorders of labyrinth
386.9 Unspecified vertiginous syndromes and labyrinthine disorders
388.5 Disorders of acoustic nerve
Acoustic neuritis
Degeneration of acoustic or
eighth nerve
Disorder of acoustic or
eighth nerve
Excludes: acoustic
neuroma (225.1)
syphilitic acoustic neuritis (094.86)
Discharging ear NOS
388.61 Cerebrospinal fluid otorrhea
Excludes: cerebrospinal
fluid rhinorrhea (349.81)
Conductive deafness
389.00 Conductive hearing loss, unspecified
389.01 Conductive hearing loss, external ear
389.02 Conductive hearing loss, tympanic membrane
389.03 Conductive hearing loss, middle ear
389.04 Conductive hearing loss, inner ear
389.08 Conductive hearing loss of combined types
389.1 Sensorineural hearing loss
Perceptive hearing loss or
deafness
Excludes: abnormal
auditory perception (388.40-388.44)
psychogenic deafness (306.7)
389.10 Sensorineural hearing loss, unspecified
389.18 Sensorineural hearing loss of combined types
389.2 Mixed conductive and sensorineural hearing loss
Deafness or hearing loss of
type classifiable to 389.0 with type classifiable to 389.1
389.7 Deaf mutism, not elsewhere classifiable
Deaf, nonspeaking
389.8 Other specified forms of hearing loss
389.9 Unspecified hearing loss
Deafness NOS
CEREBROVASCULAR DISEASE (430-438)
Includes: with mention of hypertension
(conditions classifiable to 401-405)
Use additional code to
identify presence of hypertension
Excludes: any condition classifiable to 430-434, 436, 437 occurring during
pregnancy, childbirth, or the puerperium, or specified as puerperal (674.0)
iatrogenic cerebrovascular infarction or hemorrhage (997.02)
Meningeal
hemorrhage
Ruptured:
berry aneurysm
(congenital) cerebral aneurysm NOS
Excludes: syphilitic
ruptured cerebral aneurysm (094.87)
Hemorrhage (of):
basilar
bulbar
cerebellar
cerebral
cerebromeningeal
cortical
internal capsule
intrapontine
pontine
subcortical
ventricular
Rupture of blood vessel in
brain
432.0 Nontraumatic extradural hemorrhage
Nontraumatic epidural
hemorrhage
Subdural hematoma,
nontraumatic
432.9 Unspecified intracranial hemorrhage
Intracranial hemorrhage NOS
The following fifth-digit
subclassification is for use with category 433:
0 without mention of cerebral infarction
1 with cerebral infarction
Includes: embolism of basilar, carotid, and
vertebral arteries
narrowing of basilar, carotid, and vertebral arteries
obstruction of basilar, carotid, and vertebral arteries
thrombosis of basilar, carotid, and vertebral arteries
Excludes: insufficiency
NOS of precerebral arteries (435.0-435.9)
433.8 Other specified precerebral artery
433.9 Unspecified precerebral artery
Precerebral artery NOS
The following fifth-digit
subclassification is for use with category 434:
0 without mention of cerebral infarction
1 with cerebral infarction
Thrombosis of cerebral
arteries
434.9 Cerebral artery occlusion, unspecified
Includes: cerebrovascular insufficiency (acute)
with transient focal neurological signs and symptoms
insufficiency of basilar, carotid, and vertebral arteries
spasm of cerebral arteries
Excludes: acute
cerebrovascular insufficiency NOS (437.1)
that due to any condition classifiable to 433
(433.0-433.9)
435.1 Vertebral artery syndrome
435.2 Subclavian steal syndrome
435.3 Vertebrobasilar artery syndrome
435.8 Other specified transient cerebral ischemias
435.9 Unspecified transient cerebral ischemia
Impending cerebrovascular
accident
Intermittent cerebral
ischemia
Transient ischemic attack
[TIA]
Apoplexy, apoplectic:
NOS
attack
cerebral
seizure
Cerebral seizure
Excludes: any
condition classifiable to categories 430-435
cerebrovascular accident (434.91)
CVA (ischemic)
(434.91)
embolic (434.11)
hemorrhagic (430, 431, 432.0-432.9)
thrombotic (434.01)
postoperative cerebrovascular accident (997.02)
stroke (ischemic) (434.91)
embolic (434.11)
hemorrhagic (430, 431, 432.0-432.9)
thrombotic (434.01)
437.0 Cerebral atherosclerosis
Atheroma of cerebral
arteries
Cerebral arteriosclerosis
437.1 Other generalized ischemic cerebrovascular disease
Acute cerebrovascular
insufficiency NOS
Cerebral ischemia (chronic)
437.2 Hypertensive encephalopathy
437.3 Cerebral aneurysm, nonruptured
Internal carotid artery,
intracranial portion
Internal carotid artery NOS
Excludes: congenital
cerebral aneurysm, nonruptured (747.81)
internal carotid artery, extracranial portion (442.81)
437.6 Nonpyogenic thrombosis of intracranial venous sinus
Excludes: pyogenic
(325)
437.7 Transient global amnesia
Cerebrovascular disease or
lesion NOS
Note: This category is to be used to indicate
conditions in 430-437 as the cause of late effects. The "late effects" include conditions
specified as such, or as sequelae, which may occur at any time after the onset
of the causal condition.
438.1 Speech and language deficits
438.10 Speech and language deficit, unspecified
438.19 Other speech and language deficits
438.20 Hemiplegia affecting unspecified side
438.21 Hemiplegia affecting dominant side
438.22 Hemiplegia affecting nondominant side
438.3 Monoplegia of upper limb
438.30 Monoplegia of upper limb affecting unspecified side
438.31 Monoplegia of upper limb affecting dominant side
438.32 Monoplegia of upper limb affecting nondominant side
438.4 Monoplegia of lower limb
438.40 Monoplegia of lower limb affecting unspecified side
438.41 Monoplegia of lower limb affecting dominant side
438.42 Monoplegia of lower limb affecting nondominant side
438.5 Other paralytic syndrome
Use additional code to
identify type of paralytic syndrome, such as:
locked-in state (344.81)
quadriplegia (344.00-344.09)
Excludes: late
effects of cerebrovascular accident with:
hemiplegia/hemiparesis (438.20-438.22)
monoplegia of lower limb (438.40-438.42)
monoplegia of upper limb (438.40-438.42)
438.50 Other paralytic syndrome affecting unspecified side
438.51 Other paralytic syndrome affecting dominant side
438.52 Other paralytic syndrome affecting nondominant side
438.53 Other paralytic syndrome, bilateral
438.6 Alterations of sensations
Use additional
code to identify the altered sensation
Use additional
code to identify the visual disturbance
438.8 Other late effects of cerebrovascular disease
Facial droop
438.89 Other late effects of cerebroascular disease
Use additional
code to identify the late effect
438.9 Unspecified late effects of cerebrovascular disease
DISEASES OF ARTERIES, ARTERIOLES, AND CAPILLARIES (440-448)
Raynaud's:
disease
phenomenon (secondary)
Use additional code to
identify gangrene (785.4)
443.1 Thromboangiitis obliterans [Buerger's disease]
Presenile gangrene
443.2 Other arterial dissection
443.21 Dissection of carotid artery
443.24 Dissection of vertebral artery
443.29 Dissection of other artery
443.8 Other specified peripheral vascular diseases
Disseminated necrotizing
periarteritis
Necrotizing angiitis
Panarteritis (nodosa)
Periarteritis (nodosa)
446.1 Acute febrile mucocutaneous lymph node syndrome [MCLS]
Kawasaki disease
446.2 Hypersensitivity angiitis
Excludes: antiglomerular
basement membrane disease without pulmonary hemorrhage (583.89)
446.20 Hypersensitivity angiitis, unspecified
Antiglomerular basement
membrane antibody-mediated nephritis with pulmonary hemorrhage
Use additional code to
identify renal disease (583.81)
446.29 Other specified hypersensitivity angiitis
446.4 Wegener's granulomatosis
Necrotizing respiratory granulomatosis
Wegener's syndrome
Cranial arteritis
Horton's disease
Temporal arteritis
446.6 Thrombotic microangiopathy
Moschcowitz's syndrome
Thrombotic thrombocytopenic
purpura
Aortic arch arteritis
Pulseless disease
Aortitis NOS
Endarteritis NOS
Excludes: arteritis,
endarteritis:
aortic arch (446.7)
cerebral (437.4)
coronary (414.00-414.07)
deformans (440.0-440.9)
obliterans (440.0-440.9)
pulmonary (417.8)
senile (440.0-440.9)
polyarteritis NOS (446.0)
syphilitic aortitis (093.1)
447.8 Other specified disorders of arteries and arterioles
Fibromuscular hyperplasia
of arteries, except renal
447.9 Unspecified disorders of arteries and arterioles
448.0 Hereditary hemorrhagic telangiectasia
Rendu-Osler-Weber disease
Includes: endophlebitis
inflammation, vein
periphlebitis
suppurative phlebitis
Use additional E
code to identify drug if drug-induced
Excludes: that
complicating:
abortion (634-638 with .7, 639.8)
ectopic or molar pregnancy (639.8)
pregnancy, childbirth, or the puerperium (671.0-671.9)
that due to or following:
implant or catheter device (996.61-996.62)
infusion, perfusion, or transfusion (999.2)
Excludes: intracranial
venous sinus (325)
nonpyogenic (437.6)
portal (vein) (572.1)
11. COMPLICATIONS OF PREGNANCY, CHILDBIRTH, AND THE PUERPERIUM (630-677)
Use additional code from
category 639 to identify any complications
ARTHROPATHIES AND RELATED DISORDERS (710-719)
Excludes: disorders of spine (720.0-724.9)
Includes: all collagen diseases whose effects
are not mainly confined to a single system
Excludes: those
affecting mainly the cardiovascular system, i.e., polyarteritis nodosa and
allied conditions (446.0-446.7)
710.0 Systemic lupus erythematosus
Disseminated lupus
erythematosus
Libman-Sacks disease
Use additional code to
identify manifestation, as:
endocarditis (424.91)
nephritis (583.81)
chronic (582.81)
nephrotic syndrome (581.81)
Excludes: lupus
erythematosus (discoid) NOS (695.4)
Acrosclerosis
CRST syndrome
Progressive systemic
sclerosis
Scleroderma
Use additional code to
identify manifestation, as:
lung involvement (517.2)
myopathy (359.6)
Excludes: circumscribed
scleroderma (701.0)
Keratoconjunctivitis sicca
Sjögren's disease
Poikilodermatomyositis
Polymyositis with skin
involvement
710.5 Eosinophilia myalgia syndrome
Toxic oil syndrome
Use additional E
to identify drug, if drug induced
710.8 Other specified diffuse diseases of connective tissue
Multifocal fibrosclerosis
(idiopathic) NEC
Systemic fibrosclerosing
syndrome
710.9 Unspecified diffuse connective tissue disease
Collagen disease NOS
Excludes: rheumatic
fever (390)
rheumatoid arthritis of spine NOS (720.0)
Arthritis or polyarthritis:
atrophic
rheumatic (chronic)
Use additional code to
identify manifestation, as:
myopathy (359.6)
polyneuropathy (357.1)
Excludes: curvature of spine (737.0-737.9)
osteochondrosis of spine (juvenile) (732.0) adult (732.8)
Rheumatioid arthritis of
spine NOS
Spondylitis:
Marie-Strümpell
rheumatoid
Disorder of peripheral
ligamentous or muscular attachments of spine
Romanus lesion
720.2 Sacroiliitis, not elsewhere classified
Inflammation of sacroiliac
joint NOS
720.8 Other inflammatory spondylopathies
720.81 Inflammatory spondylopathies in diseases classified elsewhere
Code first underlying
disease, as:
tuberculosis (015.0)
720.9 Unspecified inflammatory spondylopathy
Spondylitis NOS
721.0 Cervical spondylosis without myelopathy
Cervical or cervicodorsal:
arthritis
osteoarthritis
spondylarthritis
721.1 Cervical spondylosis with myelopathy
Anterior spinal artery
compression syndrome
Spondylogenic compression
of cervical spinal cord
Vertebral artery
compression syndrome
721.2 Thoracic spondylosis without myelopathy
Thoracic:
arthritis
osteoarthritis
spondylarthritis
721.3 Lumbosacral spondylosis without myelopathy
Lumbar or lumbosacral:
arthritis
osteoarthritis
spondylarthritis
721.4 Thoracic or lumbar spondylosis with myelopathy
Spondylogenic compression
of thoracic spinal cord
Spondylogenic compression
of lumbar spinal cord
721.9 Spondylosis of unspecified site
721.90 Without mention of myelopathy
Spinal:
arthritis (deformans) (degenerative) (hypertrophic)
osteoarthritis NOS
Spondylarthrosis NOS
Spondylogenic compression of spinal cord NOS
722.0 Displacement of cervical intervertebral disc without myelopathy
Neuritis (brachial) or
radiculitis due to displacement or rupture of cervical intervertebral disc
Any condition classifiable
to 722.2 of the cervical or cervicothoracic intervertebral disc
722.1 Displacement of thoracic or lumbar intervertebral disc without myelopathy
722.10 Lumbar intervertebral disc without myelopathy
Lumbago or sciatica due to
displacement of intervertebral disc
Neuritis or radiculitis due
to displacement or rupture of lumbar intervertebral disc
Any condition classifiable
to 722.2 of the lumbar or lumbosacral intervertebral disc
722.11 Thoracic intervertebral disc without myelopathy
Any condition classifiable
to 722.2 of thoracic intervertebral disc
722.2 Displacement of intervertebral disc, site unspecified, without myelopathy
Discogenic syndrome NOS
Herniation of nucleus
pulposus NOS
Intervertebral disc NOS:
extrusion
prolapse
protrusion
rupture
Neuritis or radiculitis due
to displacement or rupture of intervertebral disc
722.4 Degeneration of cervical intervertebral disc
Degeneration of
cervicothoracic intervertebral disc
722.5 Degeneration of thoracic or lumbar intervertebral disc
722.51 Thoracic or thoracolumbar intervertebral disc
722.52 Lumbar or lumbosacral intervertebral disc
722.6 Degeneration of intervertebral disc, site unspecified
Degenerative disc disease
NOS
Narrowing of intervertebral
disc or space NOS
722.7 Intervertebral disc disorder with myelopathy
722.8 Postlaminectomy syndrome
722.9 Other and unspecified disc disorder
Calcification of
intervertebral cartilage or disc Discitis
Excludes: conditions
due to:
intervertebral disc disorders (722.0-722.9)
spondylosis (721.0-721.9)
723.0 Spinal stenosis of cervical region
Pain in neck
Barré-Liéou syndrome
Posterior cervical
sympathetic syndrome
723.3 Cervicobrachial syndrome (diffuse)
723.4 Brachia neuritis or radiculitis NOS
Cervical radiculitis
Radicular syndrome of upper
limbs
723.5 Torticollis, unspecified
Contracture of neck
Excludes: congenital
(754.1)
due to birth injury (767.8)
hysterical (300.11)
ocular torticollis (781.93)
psychogenic (306.0)
spasmodic (333.83)
traumatic, current (847.0)
723.6 Panniculitis specified as affecting neck
723.7 Ossification of posterior longitudinal ligament in cervical region
723.8 Other syndromes affecting cervical region
Cervical syndrome NEC
Klippel's disease
Occipital neuralgia
723.9 Unspecified musculoskeletal disorders and symptoms referable to neck
Cervical (region) disorder
NOS
Excludes: collapsed
vertebra (code to cause, e.g., osteoporosis, 733.00-733.09)
conditions due to:
intervertebral disc disorders (722.0-722.9)
spondylosis (721.0-721.9)
724.0 Spinal stenosis, other than cervical
724.00 Spinal stenosis, unspecified region
Low back pain
Low back syndrome
Lumbalgia
Neuralgia or neuritis of
sciatic nerve
Excludes: specified
lesion of sciatic nerve (355.0)
724.4 Thoracic or lumbosacral neuritis or radiculitis, unspecified
Radicular syndrome of lower
limbs
Vertebrogenic (pain)
syndrome NOS
Ankylosis, lumbosacral or
sacroiliac (joint)
Instability, lumbosacral or
sacroiliac (joint)
724.70 Unspecified disorder of coccyx
724.71 Hypermobility of coccyx
Coccygodynia
724.8 Other symptoms referable to back
Ossification of posterior
longitudinal ligament NOS
Panniculitis specified as
sacral or affecting back
724.9 Other unspecified back disorders
Ankylosis of spine NOS
Compression of spinal nerve
root NEC
Spinal disorder NOS
Excludes: sacroiliitis
(720.2)
RHEUMATISM, EXCLUDING THE BACK (725-729)
Includes: disorders of muscles and tendons and
their attachments, and of other soft tissues
Note: Enthesopathies are disorders of peripheral
ligamentous or muscular attachments.
Excludes: enthesopathies
(726.0-726.9)
muscular dystrophies (359.0-359.1)
myoneural disorders (358.00-358.9)
myopathies (359.2-359.9)
old disruption of ligaments of knee (717.81-717.89)
Myositis:
purulent
suppurative
Excludes: myositis:
epidemic (074.1)
interstitial (728.81)
myoneural disorder (358.00-358.9)
syphilitic (095.6)
tropical (040.81)
728.1 Muscular calcification and ossification
728.10 Calcification and ossification, unspecified
Massive calcification
(paraplegic)
728.11 Progressive myositis ossificans
728.12 Traumatic myositis ossifications
Myisitis ossificans
(circumscripta)
Polymyositis ossificans
728.2 Muscular wasting and disuse atrophy, not elsewhere classified
Amyotrophia NOS
Myofibrosis
Excludes: neuralgic
amyotrophy (353.5)
pelvic muscle wasting and disuse atrophy (618.83)
progressive muscular atrophy (335.0-335.9)
728.3 Other specific muscle disorders
Arthrogryposis
Immobility syndrome
(paraplegic)
Excludes: arthrogryposis
multiplex congenita (754.89)
stiff-man syndrome (333.91)
728.6 Contracture of palmar fascia
Dupuytren's contracture
728.8 Other disorders of muscle, ligament, and fascia
728.82 Foreign body granuloma of muscle
Talc granuloma of muscle
728.83 Rupture of muscle, nontraumatic
Use additional code to
identify:
infectious organism (041.00-041.89)
gangrene (785.4), if applicable
Excludes: generalized
weakness (780.79)
Eosinophilic fasciitis
Use additional E
code to identify drug, if drug induced
728.9 Unspecified disorder of muscle, ligament, and fascia
Excludes: acroparesthesia
(443.89)
carpal tunnel syndrome (354.0)
disorders of the back (720.0-724.9)
entrapment syndromes (354.0-355.9)
palindromic rheumatism (719.3)
periarthritis (726.0-726.9)
psychogenic rheumatism (306.0)
729.0 Rheumatism, unspecified and fibrositis
729.1 Myalgia and myositis, unspecified
Fibromyositis NOS
729.2 Neuralgia, neuritis, and radiculitis, unspecified
Excludes: brachia
radiculitis (723.4)
cervical radiculitis (723.4)
lumbosacral radiculitis (724.4)
mononeuritis (354.0-355.9)
radiculitis due to intervertebral disc involvement
(722.0-722.2,722.7)
sciatica (724.3)
Excludes: necrotizing
fasciitis (728.86)
nodular fasciitis (728.79)
729.8 Other musculoskeletal symptoms referable to limbs
Excludes: abnormality
of gait (781.2)
tetany (781.7)
transient paralysis of limb (781.4)
729.9 Other and unspecified disorders of soft tissue
Polyalgia
Excludes: congenital
(754.2)
737.0 Adolescent postural kyphosis
Excludes: osteochondrosis
of spine (juvenile) (732.0)
adult (732.8)
737.10 Kyphosis (acquired) (postural)
737.11 Kyphosis due to radiation
737.12 Kyphosis, postlaminectomy
Excludes: that
associated with conditions classifiable elsewhere (737.41)
737.20 Lordosis (acquired) (postural)
737.21 Lordosis, postlaminectomy
737.22 Other postsurgical lordosis
Excludes: that
associated with conditions classifiable elsewhere (737.42)
737.3 Kyphoscoliosis and scoliosis
737.30 Scoliosis [and kyphoscoliosis], idiopathic
737.31 Resolving infantile idiopathic scoliosis
737.32 Progressive infantile idiopathic scoliosis
737.33 Scoliosis due to radiation
Excludes: that
associated with conditions classifiable elsewhere (737.43)
that in kyphoscoliotic heart disease (416.1)
737.4 Curvature of spine associated with other conditions
Code first associated
condition, as:
Charcot-Marie-Tooth
disease (356.1)
mucopolysaccharidosis (277.5)
neurofibromatosis (237.7)
osteitis deformans (731.0)
osteitis fibrosa cystica (252.01)
osteoporosis (733.00-733.09)
poliomyelitis (138)
tuberculosis [Pott's curvature] (015.0)
737.40 Curvature of spine, unspecified
737.8 Other curvatures of spine
737.9 Unspecified curvature of spine
Curvature of spine
(acquired) (idiopathic) NOS
Hunchback, acquired
Excludes: deformity
of spine NOS (738.5)
738.2 Acquired deformity of neck
738.4 Acquired spondylolisthesis
Degenerative
spondylolisthesis
Spondylolysis, acquired
Excludes: congenital
(756.12)
738.5 Other acquired deformity of back or spine
Deformity of spine NOS
Excludes: curvature
of spine (737.0-737.9)
Acrania
Amyelencephalus
Hemianencephaly
Hemicephaly
Excludes: spina
bifida occulta (756.17)
The following fifth-digit
subclassification is for use with category 741:
0 unspecified region
1 cervical region
2 dorsal (thoracic) region
3 lumbar region
Arnold-Chiari syndrome,
type II
Chiari malformation, type
II
Any condition classifiable
to 741.9 with any condition classifiable to 742.3
741.9 Without mention of hydrocephalus
Hydromeningocele (spinal)
Hydromyelocele
Meningocele (spinal)
Meningomyelocele
Myelocele
Myelocystocele
Rachischisis
Spina bifida (aperta)
Syringomyelocele
Encephalocystocele
Encephalomyelocele
Hydroencephalocele
Hydromeningocele, cranial
Meningocele, cerebral
Meningoencephalocele
Hydromicrocephaly
Micrencephaly
742.2 Reduction deformities of brain
Absence of part of brain
Agenesis of part of brain
Agyria
Aplasia of part of brain
Arhinencephaly
Holoprosencephaly
Hypoplasia of part of brain
Microgyria
742.3 Congenital hydrocephalus
Aqueduct of Sylvius:
anomaly
obstruction, congenital
stenosis
Atresia of foramina of
Magendie and Luschka
Hydrocephalus in newborn
Excludes: hydrocephalus:
acquired (331.3-331.4)
due to congenital toxoplasmosis (771.2)
with any condition classifiable to 741.9 (741.0)
742.4 Other specified anomalies of brain
Congenital cerebral cyst
Macroencephaly
Macrogyria
Megalencephaly
Multiple anomalies of brain
NOS
Porencephaly
Ulegyria
742.5 Other specified anomalies of spinal cord
Hydrorhachis
Amyelia
Atelomyelia
Congenital anomaly of
spinal meninges
Defective development of
cauda equina
Hypoplasia of spinal cord
Myelatelia
Myelodysplasia
742.8 Other specified anomalies of nervous system
Agenesis of nerve
Displacement of brachial
plexus
Familial dysautonomia
Jaw-winking syndrome
Marcus-Gunn syndrome
Riley-Day syndrome
Excludes: neurofibromatosis
(237.7)
742.9 Unspecified anomaly of brain, spinal cord, and nervous system
Anomaly of brain, nervous
system, and spinal cord
Congenital, of brain,
nervous system, and spinal cord:
disease of brain, nervous system, and spinal cord
lesion of brain, nervous system, and spinal cord
Deformity of brain, nervous
system, and spinal cord
780.0 Alteration of consciousness
Excludes: coma:
diabetic (250.2-250.3)
hepatic (572.2)
originating in the perinatal period (779.2)
780.02 Transient alteration of awareness
780.03 Persistent vegetative state
Drowsiness
Semicoma
Unconsciousness
Somnolence
Stupor
Hallucinations:
NOS
auditory
gustatory
olfactory
tactile
Excludes: those
associated with mental disorders, as functional psychoses (295.0-298.9)
organic brain syndromes (290.0-294.9, 310.0-310.9)
visual hallucinations (368.16)
Blackout
Fainting
(Near) (Pre)syncope
Vasovagal attack
Excludes: carotid
sinus syncope (337.0)
heat syncope (992.1)
neurocirculatory asthenia (306.2)
orthostatic hypotension (458.0)
shock NOS (785.50)
Excludes: convulsions:
epileptic (345.10-345.91)
in newborn (779.0)
Febrile seizures
Convulsive disorder NOS
Fits NOS
Seizures NOS
Light-headedness
Vertigo NOS
Excludes: Ménière's
disease and other specified vertiginous syndromes (386.0-386.9)
Excludes: that
of nonorganic origin (307.40-307.49)
780.50 Sleep disturbance, unspecified
780.51 Insomnia with sleep apnea
Insomnia NOS
780.53 Hypersomnia with sleep apnea
Hypersomnia NOS
780.55 Disruptions of 24-hour sleep-wake cycle
Inversion of sleep rhythm
Irregular sleep-wake rhythm
NOS
Non-24-hour sleep-wake
rhythm
780.56 Dysfunctions associated with sleep stages or arousal from sleep
780.57 Other and unspecified sleep apnea
780.58 Sleep related movement disorder
Periodic limb movement disorder
Excludes: restless leg syndrome (333.99)
Excludes: debility,
unspecified (799.3)
fatigue (during):
combat (308.0-308.9)
heat (992.6)
pregnancy (646.8)
neurasthenia (300.5)
senile asthenia (797)
780.71 Chronic fatigue syndrome
780.79 Other malaise and fatigue
Asthenia NOS
Lethargy
Postviral (asthenic)
syndrome
Tiredness
780.8 Generalized hyperhidrosis
Diaphoresis
Excessive sweating
Secondary hyperhidrosis
Excludes: focal (localized) (primary) (secondary)
hyperhidrosis (705.21-705.22)
Frey's syndrome
(705.22)
Amnesia (retrograde)
Memory loss NOS
Excludes: mild
memory disturbance due to organic brain damage (310.1)
transient global amnesia (437.7)
Chill(s) NOS
Generalized pain
Hypothermia, not associated
with low environmental temperature
Excludes: depression
NOS (311)
disorders specifically relating to:
back (724.0-724.9)
hearing (388.0-389.9)
joint (718.0-719.9)
limb (729.0-729.9)
neck (723.0-723.9)
vision (368.0-369.9)
pain in limb (729.5)
781.0 Abnormal involuntary movements
Abnormal head movements
Fasciculation
Spasms NOS
Tremor NOS
Excludes: abnormal
reflex (796.1)
chorea NOS (333.5)
infantile spasms (345.60-345.61)
spastic paralysis (342.1, 343.0-344.9)
specified movement disorders classifiable to 333 (333.0-333.9)
that of nonorganic origin (307.2-307.3)
781.1 Disturbances of sensation of smell and taste
Anosmia
Parageusia
Parosmia
Gait:
ataxic
paralytic
spastic
staggering
Excludes: ataxia:
NOS (781.3)
locomotor (progressive) (094.0)
difficulty in walking (719.7)
Ataxia NOS
Muscular incoordination
Excludes: ataxic
gait (781.2)
cerebellar ataxia (334.0-334.9)
difficulty in walking (719.7)
vertigo NOS (780.4)
781.4 Transient paralysis of limb
Monoplegia, transient NOS
Excludes: paralysis
(342.0-344.9)
Dupre's syndrome
Meningism
Carpopedal spasm
Excludes: tetanus
neonatorum (771.3)
tetany:
hysterical (300.11)
newborn (hypocalcemic) (775.4)
parathyroid (252.1)
psychogenic (306.0)
781.8 Neurologic neglect syndrone
Asomatognosia
Hemi-akinesia
Hemi-inattention
Hemispatial neglect
Left-sided neglect
Sensory extinction
Sensory neglect
Visuospatial neglect
781.9 Other symptoms involving nervous and musculoskeletal systems
Excludes: osteoporosis
(733.00-733.09)
Facial droop
Excludes: facial
weakness due to late effect of cerebrovascular accident (438.83)
781.99 Other symptoms involving nervous and musculoskeletal systems
Excludes: symptoms
relating to breast (611.71-611.79)
782.0 Disturbance of skin sensation
Anesthesia of skin
Burning or prickling
sensation
Hyperesthesia
Hypoesthesia
Numbness
Paresthesia
Tingling
Excludes: encephalopathy
NOS (348.30)
specific symptoms involving neck classifiable to 723
(723.0-723.9)
Facial pain
Pain in head NOS
Excludes: atypical
face pain (350.2)
migraine (346.0-346.9)
tension headache (307.81)
Excludes: dysphagia
(787.2)
neck pain (723.1)
sore throat (462)
chronic (472.1)
784.2 Swelling, mass, or lump in head and neck
Space-occupying lesion,
intracranial NOS
Excludes: developmental
aphasia (315.31)
784.40 Voice disturbance, unspecified
Loss of voice
Change in voice
Dysphonia
Hoarseness
Hypernasality
Hyponasality
784.5 Other speech disturbance
Dysarthria
Dysphasia
Slurred speech
Excludes: stammering
and stuttering (307.0)
that of nonorganic origin (307.0, 307.9)
784.6 Other symbolic dysfunction
Excludes: developmental
learning delays (315.0-315.9)
784.60 Symbolic dysfunction, unspecified
Alexia (with agraphia)
Acalculia
Agnosia
Agraphia NOS
Apraxia
788.20 Retention of urine, unspecified
788.21 Incomplete bladder emptying
788.29 Other specified retention of urine
Excludes: that
of nonorganic origin (307.6)
Code, if applicable,
any causal condition first, such as:
congenital ureterocele (753.23)
genital prolapse (618.00-618.9)
788.30 Urinary incontinence, unspecified
Enuresis NOS
788.32 Stress incontinence, male
Excludes: stress
incontinence, female (625.6)
788.33 Mixed incontinence (female) (male)
Urge and stress
788.34 Incontinence without sensory awareness
788.39 Other urinary incontinence
788.4 Frequency of urination and polyuria
Frequency of micturition
794.0 Brain and central nervous system
794.00 Abnormal function study, unspecified
794.01 Abnormal echoencephalogram
794.02 Abnormal electroencephalogram [EEG]
Abnormal brain scan
794.1 Peripheral nervous system and special senses
794.10 Abnormal response to nerve stimulation, unspecified
794.11 Abnormal retinal function studies
Abnormal electroretinogram
[ERG]
794.12 Abnormal electro-oculogram [EOG]
794.13 Abnormal visually evoked potential
794.14 Abnormal oculomotor studies
794.15 Abnormal auditory function studies
794.16 Abnormal vestibular function studies
794.17 Abnormal electromyogram [EMG]
Excludes: that
of eye (794.14)
Old age
Senescence
Senile asthenia
Senile:
debility
exhaustion
Excludes: senile
psychoses (290.0-290.9)
The following fifth-digit
subclassification is for use with the appropriate codes in categories 800, 801,
803, and 804:
0 unspecified state of consciousness
1 with no loss of consciousness
2 with brief [less than one hour] loss of consciousness
3 with moderate [1-24 hours] loss of consciousness
4 with prolonged [more than 24 hours] loss of consciousness and return
to pre-existing conscious level
5 with prolonged [more than 24 hours] loss of consciousness, without
return to pre-existing conscious level
Use fifth-digit 5 to
designate when a patient is unconscious and dies before regaining
consciousness, regardless of the duration of the loss of consciousness
6 with loss of consciousness of unspecified duration
9 with concussion, unspecified
Requires
fifth digit. See beginning of
section 800-804 for codes and definitions.
Includes: frontal bone
parietal bone
800.0 Closed without mention of intracranial injury
800.1 Closed with cerebral laceration and contusion
800.2 Closed wtih subarachnoid, subdural, and extradural hemorrhage
800.3 Closed with other and unspecified intracranial hemorrhage
800.4 Closed with intracranialinjury of other and unspecified nature
800.5 Open without mention of intracranial injury
800.6 Open with cerebral laceration and contusion
800.7 Open with subarachnoid, subdural, and extradural hemorrhage
800.8 Open with other and unspecified intracranial hemorrhage
800.9 Open with intracranial injury of other and unspecified nature
802.4 Malar and maxillary bones, closed
Superior maxilla
Upper jaw (bone)
Zygoma
Zygomatic arch
802.5 Malar and maxillary bones, open
802.6 Orbital floor (blow-out), closed
802.7 Orbital floor (blow-out), open
802.8 Other facial bones, closed
Alveolus
Orbit:
NOS
part other than roof or floor
Palate
Excludes: orbital:
floor (802.6)
roof (801.0-801.9)
802.9 Other facial bones, open
Requires
fifth digit. See beginning of
section 800-804 for codes and definitions.
Includes: skull NOS
skull multiple NOS
803.0 Closed without mention of intracranial injury
803.1 Closed with cerebral laceration and contusion
803.2 Closed with subarachnoid, subdural, and extradural hemorrhage
803.3 Closed with other and unspecified intracranial hemorrhage
803.4 Closed with intracranial injury of other and unspecified nature
803.5 Open without mention of intracranial injury
803.6 Open with cerebral laceration and contusion
803.7 Open with subarachnoid, subdural, and extradural hemorrhage
803.8 Open with other and unspecified intracranial hemorrhage
803.9 Open with intracranial injury of other and unspecified nature
Requires
fifth digit. See beginning of
section 800-804 for codes and definitions.
804.0 Closed without mention of intracranial injury
804.1 Closed with cerebral laceration and contusion
804.2 Closed with subarachnoid, subdural, and extradural hemorrhage
804.3 Closed with other and unspecified intracranial hemorrhage
804.4 Closed with intracranialinjury of other and unspecified nature
804.5 Open without mention of intracranial injury
804.6 Open with cerebral laceration and contusion
804.7 Open with subarachnoid, subdural, and extradural hemorrhage
804.8 Open with other and unspecified intracranial hemorrhage
804.9 Open with intracranial injury of other and unspecified nature
FRACTURE OF NECK AND TRUNK (805-809)
Includes: neural arch
spine
spinous process
transverse process
vertebra
The following fifth-digit
subclassification is for use with codes 805.0-805.1:
0 cervical vertebra, unspecified level
1 first cervical vertebra
2 second cervical vertebra
3 third cervical vertebra
4 fourth cervical vertebra
5 fifth cervical vertebra
6 sixth cervical vertebra
7 seventh cervical vertebra
8 multiple cervical vertebrae
Atlas
Axis
805.2 Dorsal [thoracic], closed
805.6 Sacrum and coccyx, closed
Includes: any condition classifiable to 805
with:
complete or incomplete transverse lesion (of cord)
hematomyelia
injury to:
cauda equina
nerve
paralysis
paraplegia
quadriplegia
spinal concussion
806.00 C1-C4 level with unspecified spinal cord injury
Cervical region NOS with
spinal cord injury NOS
806.01 C1-C4 level with complete lesion of cord
806.02 C1-C4 level with anterior cord syndrome
806.03 C1-C4 level with central cord syndrome
806.04 C1-C4 level with other specified spinal cord injury
C1-C4 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.05 C5-C7 level with unspecified spinal cord injury
806.06 C5-C7 level with complete lesion of cord
806.07 C5-C7 level with anterior cord syndrome
806.08 C5-C7 level with central cord syndrome
806.09 C5-C7 level with other specified spinal cord injury
C5-C7 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.10 C1-C4 level with unspecified spinal cord injury
806.11 C1-C4 level with complete lesion of cord
806.12 C1-C4 level with anterior cord syndrome
806.13 C1-C4 level with central cord syndrome
806.14 C1-C4 level with other specified spinal cord injury
C1-C4 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.15 C5-C7 level with unspecified spinal cord injury
806.16 C5-C7 level with complete lesion of cord
806.17 C5-C7 level with anterior cord syndrome
806.18 C5-C7 level with central cord syndrome
806.19 C5-C7 level with other specified spinal cord injury
C5-C7 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.2 Dorsal [thoracic], closed
806.20 T1-T6 level with unspecified spinal cord injury
Thoracic region NOS with
spinal cord injury NOS
806.21 T1-T6 level with complete lesion of cord
806.22 T1-T6 level with anterior cord syndrome
806.23 T1-T6 level with central cord syndrome
806.24 T1-T6 level with other specified spinal cord injury
T1-T6 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.25 T7-T12 level with unspecified spinal cord injury
806.26 T7-T12 level with complete lesion of cord
806.27 T7-T12 level with anterior cord syndrome
806.28 T7-T12 level with central cord syndrome
806.29 T7-T12 level with other specified spinal cord injury
T7-T12 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.30 T1-T6 level with unspecified spinal cord injury
806.31 T1-T6 level with complete lesion of cord
806.32 T1-T6 level with anterior cord syndrome
806.33 T1-T6 level with central cord syndrome
806.34 T1-T6 level with other specified spinal cord injury
T1-T6 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.35 T7-T12 level with unspecified spinal cord injury
806.36 T7-T12 level with complete lesion of cord
806.37 T7-T12 level with anterior cord syndrome
806.38 T7-T12 level with central cord syndrome
806.39 T7-T12 level with other specified spinal cord injury
T7-T12 level
with:
incomplete spinal cord lesion NOS
posterior cord syndrome
806.6 Sacrum and coccyx, closed
806.60 With unspecified spinal cord injury
806.61 With complete cauda equina lesion
806.62 With other cauda equina injury
806.69 With other spinal cord injury
806.70 With unspecified spinal cord injury
806.71 With complete cauda equina lesion
806.72 With other cauda equina injury
806.79 With other spinal cord injury
839.0 Cervical vertebra, closed
Cervical spine
Neck
839.00 Cervical vertebra, unspecified
839.01 First cervical vertebra
839.02 Second cervical vertebra
839.03 Third cervical vertebra
839.04 Fourth cervical vertebra
839.05 Fifth cervical vertebra
839.06 Sixth cervical vertebra
839.07 Seventh cervical vertebra
839.08 Multiple cervical vertebrae
839.10 Cervical vertebra, unspecified
839.11 First cervical vertebra
839.12 Second cervical vertebra
839.13 Third cervical vertebra
839.14 Fourth cervical vertebra
839.15 Fifth cervical vertebra
839.16 Sixth cervical vertebra
839.17 Seventh cervical vertebra
839.18 Multiple cervical vertebrae
839.2 Thoracic and lumbar vertebra, closed
Dorsal [thoracic] vertebra
839.3 Thoracic and lumbar vertebra, open
839.40 Vertebra, unspecified site
Spine NOS
Sacroiliac (joint)
839.50 Vertebra, unspecified site
Sternoclavicular joint
Pelvis
839.8 Multiple and ill-defined, closed
Arm
Back
Hand
Multiple locations, except
fingers or toes alone
Other ill-defined locations
Unspecified location
839.9 Multiple and ill-defined, open
INTRACRANIAL INJURY, EXCLUDING THOSE WITH SKULL FRACTURE (850-854)
Excludes: intracranial injury with skull fracture (800-801 and 803-804, except .0
and .5)
open wound of head without intracranial injury
(870.0-873.9)
skull fracture alone (800-801 and 803-804 with .0, .5)
Note: The description "with open intracranial
wound," used in the fourth-digit subdivisions, includes those specified as
open or with mention of infection or foreign body.
The following fifth-digit
subclassification is for use with categories 851-854:
0 unspecified state of consciousness
1 with no loss of consciousness
2 with brief [less than one hour] loss of consciousness
3 with moderate [1-24 hours] loss of consciousness
4 with prolonged [more than 24 hours] loss of consciousness and return
to pre-existing conscious level
5 with prolonged [more than 24 hours] loss of consciousness without
return to pre-existing conscious level
Use fifth-digit 5 to
designate when a patient is unconscious and dies before regaining
consciousness, regardless of the duration of the loss of consciousness
6 with loss of consciousness of unspecified duration
9 with concussion, unspecified
Includes: commotio cerebri
Excludes: concussion
with:
cerebral laceration or contusion (851.0-851.9)
cerebral hemorrhage (852-853)
head injury NOS (959.01)
850.0 With no loss of consciousness
Concussion with mental
confusion or disorientation, without loss of consciousness
850.1 With brief loss of consciousness
Loss of consciousness for
less than one hour
850.11 With loss of consciousness of 30 minutes or less
850.12 With loss of consciousness from 31 to 59 minutes
850.2 With moderate loss of consciousness
Loss of consciousness for
1-24 hours
850.3 With prolonged loss of consciousness and return to pre-existing conscious level
Loss of consciousness for
more than 24 hours with complete recovery
850.4 With prolonged loss of consousness, without return to pre-existing conscious level
850.5 With loss of consciousness of unspecified duration
Requires
fifth digit. See beginning of
section 850-854 for codes and definitions.
851.0 Cortex (cerebral) contusion without mention of open intracranial wound
851.1 Cortex (cerebral) contusion with open intracranial wound
851.2 Cortex (cerebral) laceration without mention of open intracranial wound
851.3 Cortex (cerebral) laceration with open intracranial wound
851.4 Cerebellar or brain stem contusion without mention of open intracranial wound
851.5 Cerebellar or brain stem contusion with open intracranial wound
851.6 Cerebellar or brain stem laceration without mention of open intracranial wound
851.7 Cerebellar or brain stem laceration with open intracranial wound
851.8 Other and unspecified cerebral laceration and contusion, without mention of open intracranial wound
Brain (membrane) NOS
851.9 Other and unspecified cerebral laceration and contusion, with open intracranial wound
Requires
fifth digit. See beginning of
section 850-854 for codes and definitions.
Excludes: cerebral
contusion or laceration (with hemorrhage) (851.0-851.9)
852.0 Subarachnoid hemorrhage following injury without mention of open intracranial wound
Middle meningeal hemorrhage
following injury
852.1 Subarachnoid hemorrhage following injury with open intracranial wound
852.2 Subdural hemorrhage following injury without mention of open intracranial wound
852.3 Subdural hemorrhage following injury with open intracranial wound
852.4 Extradural hemorrhage following injury without mention of open intracranial wound
Epidural hematoma following
injury
852.5 Extradural hemorrhage following injury with open intracranial wound
Requires
fifth digit. See beginning of
section 850-854 for codes and definitions.
853.0 Without mention of open intracranial wound
Cerebral compression due to
injury
Intracranial hematoma
following injury
Traumatic cerebral
hemorrhage
853.1 With open intracranial wound
Includes: injury:
brain NOS
cavernous sinus
intracranial
Excludes: any
condition classifiable to 850-853
head injury NOS (959.01)
854.0 Without mention of open intracranial wound
854.1 With open intracranial wound
INJURY TO NERVES AND SPINAL CORD (950-957)
Includes: division of nerve
lesion in continuity (with open wound)
traumatic neuroma (with open wound)
traumatic transient paralysis (with open wound)
Excludes: accidental puncture or laceration during medical procedure (998.2)
Second cranial nerve
950.2 Injury to optic pathways
Traumatic blindness NOS
951.0 Injury to oculomotor nerve
Third cranial nerve
951.1 Injury to trochlear nerve
Fourth cranial nerve
951.2 Injury to trigeminal nerve
Fifth cranial nerve
951.3 Injury to abducens nerve
Sixth cranial nerve
Seventh cranial nerve
951.5 Injury to acoustic nerve
Auditory nerve
Eighth cranial nerve
Traumatic deafness NOS
951.6 Injury to accessory nerve
Eleventh cranial nerve
951.7 Injury to hypoglossal nerve
Twelfth cranial nerve
951.8 Injury to other specified cranial nerves
Glossopharyngeal [9th
cranial] nerve
Olfactory [1st cranial]
nerve
Pneumogastric [10th
cranial] nerve
Traumatic anosmia NOS
Vagus [10th cranial] nerve
951.9 Injury to unspecified cranial nerve
952.00 C1-C4 level with unspecified spinal cord injury
Spinal cord injury,
cervical region NOS
952.01 C1-C4 level with complete lesion of spinal cord
952.02 C1-C4 level with anterior cord syndrome
952.03 C1-C4 level with central cord syndrome
952.04 C1-C4 level with other specified spinal cord injury
Incomplete spinal cord
lesion at C1-C4 level:
NOS
with posterior cord syndrome
952.05 C5-C7 level with unspecified spinal cord injury
952.06 C5-C7 level with complete lesion of spinal cord
952.07 C5-C7 level with anterior cord syndrome
952.08 C5-C7 level with central cord syndrome
952.09 C5-C7 level with other specified spinal cord injury
Incomplete spinal cord
lesion at C5-C7 level:
NOS
with posterior cord syndrome
952.10 T1-T6 level with unspecified spinal cord injury
Spinal cord injury,
thoracic region NOS
952.11 T1-T6 level with complete lesion of spinal cord
952.12 T1-T6 level with anterior cord syndrome
952.13 T1-T6 level with central cord syndrome
952.14 T1-T6 level with other specified spinal cord injury
Incomplete spinal cord
lesion at T1-T6 level:
NOS
with posterior cord syndrome
952.15 T7-T12 level with unspecified spinal cord injury
952.16 T7-T12 level with complete lesion of spinal cord
952.17 T7-T12 level with anterior cord syndrome
952.18 T7-T12 level with central cord syndrome
952.19 T7-T12 level with other specified spinal cord injury
Incomplete spinal cord
lesion at T7-T12 level:
NOS
with posterior cord syndrome
952.8 Multiple sites of spinal cord
952.9 Unspecified site of spinal cord
Celiac ganglion or plexus
Inferior mesenteric plexus
Splanchnic nerve(s)
Stellate ganglion
954.8 Other specified nerve(s) of trunk
954.9 Unspecified nerve of trunk
955.5 Cutaneous sensory nerve, upper limb
955.7 Other specified nerve(s) of shoulder girdle and upper limb
955.8 Multiple nerves of shoulder girdle and upper limb
955.9 Unspecified nerve of shoulder girdle and upper limb
956.4 Cutaneous sensory nerve, lower limb
956.5 Other specified nerve(s) of pelvic girdle and lower limb
956.8 Multiple nerves of pelvic girdle and lower limb
956.9 Unspecified nerve of pelvic girdle and lower limb
957.0 Superficial nerves of head and neck
957.1 Other specified nerve(s)
957.8 Multiple nerves in several parts
Multiple nerve injury NOS
Nerve injury NOS