A 4 year-old boy presented with an altered gait since beginning to walk at age three, along with cognitive developmental delay.

Schizencephaly is a rare disorder of neuronal migration. Similar to porencephaly, there is a cerebrospinal fluid–filled cleft, but in contrast to porencephaly, the cleft is lined by gray matter. The cleft typically extends from the ventricle to the surface of the brain. Schizencephaly is commonly divided into types I and II. In type I, the clefts are fused (so called fused lips), whereas in type II, the clefts are open (so-called open lips). In this case, the clefts are nearly fused and would be considered type I schizencephaly. Similar to porencephaly, patients present in infancy with seizures, developmental delay or focal neurological deficits.